Q80.8 Other congenital ichthyosis

Billable ICD-10-CM code, FY2026. Exempt from present-on-admission (POA) reporting.

Applies from Q80 Congenital ichthyosis

Excludes1 (never code together)

• Refsum's disease (G60.1)

MS-DRG index

Defines the logic of DRG(s) 606-607 in MDC 09.

Approximate ICD-9-CM (GEMs)

• 757.1 Ichthyosis congenita (approximate)

Code annotations containing back-references to Q80.8

Back-references to Q80

• Type 1 Excludes: L85.0 Acquired ichthyosis ("congenital ichthyosis (Q80.-)")
• Type 1 Excludes: P83 Other conditions of integument specific to newborn ("congenital malformations of skin and integument (Q80-Q84)")

Diagnosis Index entries for Q80.8

• Hyperkeratosis › universalis congenita
• Ichthyosis (congenital) › hystrix
• Ichthyosis (congenital) › vera
• Keratosis › congenital, specified NEC

Nearby codes

• Q80.0 Ichthyosis vulgaris
• Q80.1 X-linked ichthyosis
• Q80.2 Lamellar ichthyosis
• Q80.3 Congenital bullous ichthyosiform erythroderma
• Q80.4 Harlequin fetus
• Q80.8 Other congenital ichthyosis (this code)
• Q80.9 Congenital ichthyosis, unspecified