Q81.1 Epidermolysis bullosa letalis

Billable ICD-10-CM code, FY2026. Exempt from present-on-admission (POA) reporting.

Applicable to

• Herlitz' syndrome

MS-DRG index

Defines the logic of DRG(s) 595-596 in MDC 09.

Approximate ICD-9-CM (GEMs)

• 757.39 Other specified anomalies of skin (approximate)

Code annotations containing back-references to Q81.1

Back-references to Q81

• Type 1 Excludes: L12.3 Acquired epidermolysis bullosa ("epidermolysis bullosa (congenital) (Q81.-)")
• Type 1 Excludes: P83 Other conditions of integument specific to newborn ("congenital malformations of skin and integument (Q80-Q84)")

Diagnosis Index entries for Q81.1

• Epidermolysis › bullosa (congenital) › letalis
• Herlitz' syndrome

Nearby codes

• Q81 Epidermolysis bullosa
• Q81.0 Epidermolysis bullosa simplex
• Q81.1 Epidermolysis bullosa letalis (this code)
• Q81.2 Epidermolysis bullosa dystrophica
• Q81.8 Other epidermolysis bullosa
• Q81.9 Epidermolysis bullosa, unspecified