Q82.0 Hereditary lymphedema

Billable ICD-10-CM code, FY2026. Exempt from present-on-admission (POA) reporting.

Applies from Q82 Other congenital malformations of skin

Excludes1 (never code together)

• acrodermatitis enteropathica (E83.2)
• congenital erythropoietic porphyria (E80.0)
• pilonidal cyst or sinus (L05.-)
• Sturge-Weber (-Dimitri) syndrome (Q85.89)

MS-DRG index

Defines the logic of DRG(s) 606-607 in MDC 09.

Approximate ICD-9-CM (GEMs)

• 757.0 Hereditary edema of legs

Code annotations containing back-references to Q82.0

Back-references to Q82.0

• Type 1 Excludes: I89 Other noninfective disorders of lymphatic vessels and lymph nodes ("hereditary lymphedema (Q82.0)")
• Type 1 Excludes: R60 Edema, not elsewhere classified ("hereditary edema (Q82.0)")

Back-references to Q82

• Type 1 Excludes: P83 Other conditions of integument specific to newborn ("congenital malformations of skin and integument (Q80-Q84)")

Diagnosis Index entries for Q82.0

• Disease, diseased › Meige's (chronic hereditary edema)
• Disease, diseased › Milroy's (chronic hereditary edema)
• Disease, diseased › Nonne-Milroy-Meige (chronic hereditary edema)
• Edema, edematous (infectious) (pitting) (toxic) › chronic hereditary
• Edema, edematous (infectious) (pitting) (toxic) › familial, hereditary
• Edema, edematous (infectious) (pitting) (toxic) › hereditary
• Edema, edematous (infectious) (pitting) (toxic) › legs › hereditary
• Edema, edematous (infectious) (pitting) (toxic) › Milroy's
• Elephantiasis (nonfilarial) › congenital (any site) (hereditary)
• Lymphedema (acquired) › congenital
• Lymphedema (acquired) › hereditary (chronic) (idiopathic)
• Meige-Milroy disease (chronic hereditary edema)
• Meige's syndrome
• Milroy's disease (chronic hereditary edema)
• Nonne-Milroy syndrome
• Pseudoelephantiasis neuroarthritica
• Syndrome › Nonne-Milroy-Meige
• Trophedema (congenital) (hereditary)
• Tropholymphedema

Nearby codes

• Q82 Other congenital malformations of skin
• Q82.0 Hereditary lymphedema (this code)
• Q82.1 Xeroderma pigmentosum
• Q82.2 Congenital cutaneous mastocytosis
• Q82.3 Incontinentia pigmenti
• Q82.4 Ectodermal dysplasia (anhidrotic)
• Q82.5 Congenital non-neoplastic nevus