Q82.8 Other specified congenital malformations of skin

Billable ICD-10-CM code, FY2026. Exempt from present-on-admission (POA) reporting.

Applicable to

• Abnormal palmar creases
• Accessory skin tags
• Benign familial pemphigus [Hailey-Hailey]
• Congenital poikiloderma
• Cutis laxa (hyperelastica)
• Dermatoglyphic anomalies
• Inherited keratosis palmaris et plantaris
• Keratosis follicularis [Darier-White]

Excludes1 (never code together)

• Ehlers-Danlos syndromes (Q79.6-)

Excludes2 (not included here)

• disorders of pyrophosphate metabolism (E83.82-)

Applies from Q82 Other congenital malformations of skin

Excludes1 (never code together)

• acrodermatitis enteropathica (E83.2)
• congenital erythropoietic porphyria (E80.0)
• pilonidal cyst or sinus (L05.-)
• Sturge-Weber (-Dimitri) syndrome (Q85.89)

MS-DRG index

Defines the logic of DRG(s) 606-607 in MDC 09.

Approximate ICD-9-CM (GEMs)

• 757.2 Dermatoglyphic anomalies (approximate)
• 757.39 Other specified anomalies of skin (approximate)

Code annotations containing back-references to Q82.8

Back-references to Q82.8

• Type 1 Excludes: E79 Disorders of purine and pyrimidine metabolism ("Bloom's syndrome (Q82.8)")
• Type 1 Excludes: L11.0 Acquired keratosis follicularis ("keratosis follicularis (congenital) [Darier-White] (Q82.8)")
• Type 1 Excludes: L85.1 Acquired keratosis [keratoderma] palmaris et plantaris ("inherited keratosis palmaris et plantaris (Q82.8)")

Back-references to Q82

• Type 1 Excludes: P83 Other conditions of integument specific to newborn ("congenital malformations of skin and integument (Q80-Q84)")

Diagnosis Index entries for Q82.8

• Abnormal, abnormality, abnormalities › palmar creases
• Acanthosis (acquired) (nigricans) › benign
• Acanthosis (acquired) (nigricans) › congenital
• Accessory (congenital) › skin tags
• Angiomatosis
• Anomaly, anomalous (congenital) (unspecified type) › dermatoglyphic
• Anomaly, anomalous (congenital) (unspecified type) › pigmentation › congenital
• Anomaly, anomalous (congenital) (unspecified type) › simian crease
• Bloom (-Machacek)(-Torre) syndrome
• Brugsch's syndrome
• Cutis › hyperelastica
• Cutis › verticis gyrata
• Darier (-White) disease (congenital)
• Dermatolysis (exfoliativa) (congenital)
• Dermatomegaly NEC
• Dyskeratosis › congenital
• Dysplasia › ectodermal (anhidrotic) (congenital) (hereditary) › hydrotic
• Elastic skin
• Elastoma (juvenile)
• Gyrate scalp
• Hailey-Hailey disease
• Hyperkeratosis › follicularis
• Hypoplasia, hypoplastic › focal dermal
• Hypoplasia, hypoplastic › skin
• Ichthyosis (congenital) › palmaris and plantaris
• India rubber skin
• Keratoderma, keratodermia (congenital) (palmaris et plantaris) (symmetrical)
• Keratoma › palmaris and plantaris hereditarium
• Keratosis › follicularis
• Keratosis › follicularis › congenita
• Keratosis › follicularis › spinulosa (decalvans)
• Keratosis › palmaris et plantaris (inherited) (symmetrical)
• Keratosis › vegetans
• Lax, laxity › skin (acquired) › congenital
• Lichen › congenital
• Lichen › pilaris
• Melanocytosis, neurocutaneous
• Mibelli's disease (porokeratosis)
• Naegeli's › disease
• Pachydermatocele (congenital)
• Particolored infant
• Pemphigus › benign familial (chronic)
• Pigmentation (abnormal) (anomaly) › lids, congenital
• Pigmentation (abnormal) (anomaly) › scrotum, congenital
• Poikiloderma › congenital
• Porokeratosis
• Pseudoxanthoma elasticum
• Rothmund (-Thomson) syndrome
• Siemens' syndrome (ectodermal dysplasia)
• Syndrome › telangiectasic-pigmentation-cataract

Nearby codes

• Q82.2 Congenital cutaneous mastocytosis
• Q82.3 Incontinentia pigmenti
• Q82.4 Ectodermal dysplasia (anhidrotic)
• Q82.5 Congenital non-neoplastic nevus
• Q82.6 Congenital sacral dimple
• Q82.8 Other specified congenital malformations of skin (this code)
• Q82.9 Congenital malformation of skin, unspecified