Q85.89 Other phakomatoses, not elsewhere classified
Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis. Exempt from present-on-admission (POA) reporting.
Applicable to
Peutz-Jeghers syndrome
Sturge-Weber(-Dimitri) syndrome
Applies from Q85 Phakomatoses, not elsewhere classified
Excludes1 (never code together)
ataxia telangiectasia [Louis-Bar] (G11.3)
familial dysautonomia [Riley-Day] (G90.1)
Applies from Q85.8 Other phakomatoses, not elsewhere classified
Excludes1 (never code together)
Meckel-Gruber syndrome (Q61.9)
Risk adjustment (HCC)
CMS-HCC V28: HCC 23 — Prostate, Breast, and Other Cancers and Tumors
CMS-HCC V22: HCC 12 — Breast, Prostate, and Other Cancers and Tumors
RxHCC V08: HCC 22 — Prostate, Breast, Bladder, and Other Cancers and Tumors
ESRD V24: HCC 12
MS-DRG index
Defines the logic of DRG(s) 826-828 in MDC 17.
Code annotations containing back-references to Q85.89
Back-references to Q85.89
Type 1 Excludes: L81 Other disorders of pigmentation ("Peutz-Jeghers syndrome (Q85.89)")
Type 1 Excludes: Q82 Other congenital malformations of skin ("Sturge-Weber (-Dimitri) syndrome (Q85.89)")
Diagnosis Index entries for Q85.89
Angiomatosis › encephalotrigeminal
Dimitri-Sturge-Weber disease
Kraft-Weber-Dimitri disease
Peutz-Jeghers disease or syndrome
Phakomatosis › specified NEC
Sturge (-Weber) (-Dimitri) (-Kalischer) disease or syndrome