Q87.81 Alport syndrome

Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis. Exempt from present-on-admission (POA) reporting.

Use additional code

• code to identify stage of chronic kidney disease (N18.1-N18.6)

Applies from Q87 Other specified congenital malformation syndromes affecting multiple systems

Use additional code

• code(s) to identify all associated manifestations

Applies from Q87.8 Other specified congenital malformation syndromes, not elsewhere classified

Excludes1 (never code together)

• Zellweger syndrome (E71.510)

MS-DRG index

Defines the logic of DRG(s) 564-566 in MDC 08.

Approximate ICD-9-CM (GEMs)

• 759.89 Other specified congenital anomalies (approximate)

Code annotations containing back-references to Q87.81

Back-references to Q87.81

• Type 2 Excludes: N07 Hereditary nephropathy, not elsewhere classified ("Alport's syndrome (Q87.81-)")

Back-references to Q87

• Type 1 Excludes: Q67 Congenital musculoskeletal deformities of head, face, spine and chest ("congenital malformation syndromes classified to Q87.-")
• Type 1 Excludes: Q75 Other congenital malformations of skull and face bones ("congenital malformation syndromes classified to Q87.-")
• Type 1 Excludes: Q89.7 Multiple congenital malformations, not elsewhere classified ("congenital malformation syndromes affecting multiple systems (Q87.-)")

Diagnosis Index entries for Q87.81

• Alport syndrome
• Syndrome › Alport

Nearby codes

• Q87.418 Marfan syndrome with other cardiovascular manifestations
• Q87.42 Marfan syndrome with ocular manifestations
• Q87.43 Marfan syndrome with skeletal manifestation
• Q87.5 Other congenital malformation syndromes with other skeletal changes
• Q87.8 Other specified congenital malformation syndromes, not elsewhere classified
• Q87.81 Alport syndrome (this code)
• Q87.82 Arterial tortuosity syndrome
• Q87.83 Bardet-Biedl syndrome
• Q87.84 Laurence-Moon syndrome
• Q87.85 MED13L syndrome
• Q87.86 Kleefstra syndrome