Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis. Exempt from present-on-admission (POA) reporting.
Use additional code
code, if applicable, for associated conditions such as:
cerebral palsy (G80.-)
congenital heart malformations (Q20.0-Q24.9)
developmental disorder of speech and language (F80.-)
exudative retinopathy (H35.02-)
intellectual disability (F70-F79)
microcephaly (Q02)
Applies from Q87 Other specified congenital malformation syndromes affecting multiple systems
Use additional code
code(s) to identify all associated manifestations
Applies from Q87.8 Other specified congenital malformation syndromes, not elsewhere classified
Excludes1 (never code together)
Zellweger syndrome (E71.510)
MS-DRG index
Defines the logic of DRG(s) 052-053 in MDC 01.
Code annotations containing back-references to Q87.88
Back-references to Q87
Type 1 Excludes: Q67 Congenital musculoskeletal deformities of head, face, spine and chest ("congenital malformation syndromes classified to Q87.-")
Type 1 Excludes: Q75 Other congenital malformations of skull and face bones ("congenital malformation syndromes classified to Q87.-")
Type 1 Excludes: Q89.7 Multiple congenital malformations, not elsewhere classified ("congenital malformation syndromes affecting multiple systems (Q87.-)")