Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis. Exempt from present-on-admission (POA) reporting.
Applies from Q89.8 Other specified congenital malformations
Use additional code
code(s) to identify all associated manifestations
MS-DRG index
Defines the logic of DRG(s) 564-566 in MDC 08.
Diagnosis Index entries for Q89.89
Absence (of) (organ or part) (complete or partial) › organ › or site, congenital NEC
Acardia, acardius
Acardiacus amorphus
Accessory (congenital) › genitourinary organs NEC
Acephalobrachia monster
Acephalochirus monster
Acephalogaster
Acephalostomus monster
Acephalothorax
Anomaly, anomalous (congenital) (unspecified type) › specified organ or site NEC
Atresia, atretic › organ or site NEC
CHARGE association
Cyst (colloid) (mucous) (simple) (retention) › congenital NEC
Disease, diseased › Kok
Disease, diseased › Startle
Goldberg syndrome
Hyperekplexia
Hyperexplexia
Malformation (congenital) › specified NEC
Myofibromatosis › infantile
Nephrosis, nephrotic (Epstein's) (syndrome) (congenital) › Finnish type (congenital)