Z83.42 Family history of familial hypercholesterolemia

Billable ICD-10-CM code, FY2026. Exempt from present-on-admission (POA) reporting.

Applies from Z83 Family history of other specific disorders

Excludes2 (not included here)

• contact with and (suspected) exposure to communicable disease in the family (Z20.-)

Applies from Z83.4 Family history of other endocrine, nutritional and metabolic diseases

Applicable to

• Conditions classifiable to E00-E07, E15-E88

MS-DRG index

Defines the logic of DRG(s) 795 in MDC 15.

Approximate ICD-9-CM (GEMs)

• V18.19 Family history of other endocrine and metabolic diseases (approximate)

Medicare Code Edits (MCE v43.1 (April 2026))

• Unacceptable principal diagnosis: These codes describe a circumstance which influences care but is not a current illness or injury, or capture only an underlying condition, and are unacceptable as principal diagnosis.

Code annotations containing back-references to Z83.42

Back-references to Z83

• Use Additional: Z15 Genetic susceptibility to disease ("code, if applicable, for any associated family history of the disease (Z80-Z84)")

Diagnosis Index entries for Z83.42

• History › family (of) › disease or disorder (of) › familial hypercholesterolemia
• History › family (of) › familial hypercholesterolemia

Nearby codes

• Z83.1 Family history of other infectious and parasitic diseases
• Z83.2 Family history of diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
• Z83.3 Family history of diabetes mellitus
• Z83.4 Family history of other endocrine, nutritional and metabolic diseases
• Z83.41 Family history of multiple endocrine neoplasia [MEN] syndrome
• Z83.42 Family history of familial hypercholesterolemia (this code)
• Z83.43 Family history of other disorder of lipoprotein metabolism and other lipidemias
• Z83.430 Family history of elevated lipoprotein(a)
• Z83.438 Family history of other disorder of lipoprotein metabolism and other lipidemia
• Z83.49 Family history of other endocrine, nutritional and metabolic diseases
• Z83.5 Family history of eye and ear disorders