A39.1 Waterhouse-Friderichsen syndrome
Billable ICD-10-CM code, FY2026. Acts as a Major Complication or Comorbidity (MCC) as a secondary diagnosis.
Applicable to
- Meningococcal hemorrhagic adrenalitis
- Meningococcic adrenal syndrome
Risk adjustment (HCC)
- CMS-HCC V22: HCC 23 — Other Significant Endocrine and Metabolic Disorders
- RxHCC V08: HCC 43 — Pituitary, Adrenal Gland, and Other Endocrine and Metabolic Disorders
- ESRD V24: HCC 23
MS-DRG index
Defines the logic of DRG(s) 791 in MDC 15.
Approximate ICD-9-CM (GEMs)
036.3 Waterhouse-Friderichsen syndrome, meningococcal
Code annotations containing back-references to A39.1
Back-references to A39.1
- Type 1 Excludes:
E27.1 Primary adrenocortical insufficiency ("Waterhouse-Friderichsen syndrome (A39.1)") - Type 1 Excludes:
E27.4 Other and unspecified adrenocortical insufficiency ("Waterhouse-Friderichsen syndrome (A39.1)") - Type 1 Excludes:
E35 Disorders of endocrine glands in diseases classified elsewhere ("meningococcal hemorrhagic adrenalitis (A39.1)") - Type 1 Excludes:
E35 Disorders of endocrine glands in diseases classified elsewhere ("Waterhouse-Friderichsen syndrome (A39.1)")
Diagnosis Index entries for A39.1
- Adrenalitis, adrenitis › meningococcal, hemorrhagic
- Apoplexia, apoplexy, apoplectic › adrenal
- Disease, diseased › Waterhouse-Friderichsen
- Friderichsen-Waterhouse syndrome or disease
- Infection, infected, infective (opportunistic) › meningococcal › adrenals
- Meningococcus, meningococcal › adrenalitis, hemorrhagic
- Sepsis (generalized) (unspecified organism) › adrenal hemorrhage syndrome (meningococcal)
- Syndrome › adrenal › hemorrhage (meningococcal)
- Syndrome › adrenal › meningococcic
- Syndrome › Friderichsen-Waterhouse
- Syndrome › septicemic adrenal hemorrhage
- Syndrome › Waterhouse (-Friderichsen)
- Waterhouse (-Friderichsen) syndrome or disease (meningococcal)
Nearby codes
A39 Meningococcal infectionA39.0 Meningococcal meningitisA39.1 Waterhouse-Friderichsen syndrome (this code)A39.2 Acute meningococcemiaA39.3 Chronic meningococcemiaA39.4 Meningococcemia, unspecifiedA39.5 Meningococcal heart diseaseA39.50 Meningococcal carditis, unspecified