D47.01 Cutaneous mastocytosis

Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis.

Applicable to

• Diffuse cutaneous mastocytosis
• Maculopapular cutaneous mastocytosis
• Solitary mastocytoma
• Telangiectasia macularis eruptiva perstans
• Urticaria pigmentosa

Excludes1 (never code together)

• congenital (diffuse) (maculopapular) cutaneous mastocytosis (Q82.2)
• congenital urticaria pigmentosa (Q82.2)
• extracutaneous mastocytoma (D47.09)

Applies from D47.0 Mast cell neoplasms of uncertain behavior

Excludes1 (never code together)

• congenital cutaneous mastocytosis (Q82.2)
• histiocytic neoplasms of uncertain behavior (D47.Z9)
• malignant mast cell neoplasm (C96.2-)

Risk adjustment (HCC)

• RxHCC V08: HCC 21 — Lymphomas and Other Hematologic Cancers

MS-DRG index

Defines the logic of DRG(s) 820-822 in MDC 17.

Approximate ICD-9-CM (GEMs)

• 238.5 Neoplasm of uncertain behavior of histiocytic and mast cells (approximate)

Code annotations containing back-references to D47.01

Back-references to D47.01

• Type 1 Excludes: D89.4 Mast cell activation syndrome and related disorders ("(non-congenital) cutaneous mastocytosis (D47.01)")
• Type 1 Excludes: L50 Urticaria ("urticaria pigmentosa (D47.01)")
• Type 1 Excludes: Q82.2 Congenital cutaneous mastocytosis ("cutaneous mastocytosis NOS (D47.01)")
• Type 1 Excludes: Q82.2 Congenital cutaneous mastocytosis ("diffuse cutaneous mastocytosis (with onset after newborn period) (D47.01)")
• Type 1 Excludes: Q82.2 Congenital cutaneous mastocytosis ("urticaria pigmentosa (non-congenital) (with onset after newborn period) (D47.01)")

Diagnosis Index entries for D47.01

• Mastocytoma (extracutaneous) › solitary
• Mastocytosis › cutaneous (diffuse) (maculopapular)
• Telangiectasia, telangiectasis (verrucous) › macularis eruptiva perstans
• Urticaria › pigmentosa

Nearby codes

• D47 Other neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue
• D47.0 Mast cell neoplasms of uncertain behavior
• D47.01 Cutaneous mastocytosis (this code)
• D47.02 Systemic mastocytosis
• D47.09 Other mast cell neoplasms of uncertain behavior
• D47.1 Chronic myeloproliferative disease
• D47.2 Monoclonal gammopathy
• D47.3 Essential (hemorrhagic) thrombocythemia