D58.0 Hereditary spherocytosis

Billable ICD-10-CM code, FY2026.

Applicable to

• Acholuric (familial) jaundice
• Congenital (spherocytic) hemolytic icterus
• Minkowski-Chauffard syndrome

Applies from D58 Other hereditary hemolytic anemias

Excludes1 (never code together)

• hemolytic anemia of the newborn (P55.-)

Risk adjustment (HCC)

• CMS-HCC V22: HCC 48 — Coagulation Defects and Other Specified Hematological Disorders
• ESRD V24: HCC 48

MS-DRG index

Defines the logic of DRG(s) 811-812 in MDC 16.

Approximate ICD-9-CM (GEMs)

• 282.0 Hereditary spherocytosis

Code annotations containing back-references to D58.0

Back-references to D58

• Type 1 Excludes: D57 Sickle-cell disorders ("other hemoglobinopathies (D58.-)")
• Code First: M90.5 Osteonecrosis in diseases classified elsewhere ("hemoglobinopathy (D50-D64)")
• Type 1 Excludes: R71 Abnormality of red blood cells ("anemias (D50-D64)")

Diagnosis Index entries for D58.0

• Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) › congenital › spherocytic
• Disease, diseased › hemoglobin or Hb › spherocytosis
• Jaundice (yellow) › newborn › spherocytosis (congenital)
• Spherocytosis (congenital) (familial) (hereditary)
• Spherocytosis (congenital) (familial) (hereditary) › hemoglobin disease
• Syndrome › Minkowski-Chauffard

Nearby codes

• D58 Other hereditary hemolytic anemias
• D58.0 Hereditary spherocytosis (this code)
• D58.1 Hereditary elliptocytosis
• D58.2 Other hemoglobinopathies
• D58.8 Other specified hereditary hemolytic anemias
• D58.9 Hereditary hemolytic anemia, unspecified