D66 Hereditary factor VIII deficiency

Billable ICD-10-CM code, FY2026. Acts as a Major Complication or Comorbidity (MCC) as a secondary diagnosis.

Applicable to

• Classical hemophilia
• Deficiency factor VIII (with functional defect)
• Hemophilia NOS
• Hemophilia A

Excludes1 (never code together)

• factor VIII deficiency with vascular defect (D68.0-)

Applies from D66 Hereditary factor VIII deficiency

Applicable to

• Classical hemophilia
• Deficiency factor VIII (with functional defect)
• Hemophilia NOS
• Hemophilia A

Excludes1 (never code together)

• factor VIII deficiency with vascular defect (D68.0-)

Risk adjustment (HCC)

• CMS-HCC V28: HCC 111 — Hemophilia, Male
• CMS-HCC V22: HCC 46 — Severe Hematological Disorders
• ESRD V24: HCC 46

MS-DRG index

Defines the logic of DRG(s) 813 in MDC 16.

Approximate ICD-9-CM (GEMs)

• 286.0 Congenital factor VIII disorder

Code annotations containing back-references to D66

Back-references to D66

• Type 1 Excludes: D68.0 Von Willebrand disease ("factor VIII deficiency NOS (D66)")
• Type 1 Excludes: D68.0 Von Willebrand disease ("factor VIII deficiency with functional defect (D66)")
• Code First: M36.2 Hemophilic arthropathy ("factor VIII deficiency (D66)")
• Code First: M36.2 Hemophilic arthropathy ("hemophilia (classical) (D66)")

Back-references to D66

• Type 1 Excludes: D68.0 Von Willebrand disease ("factor VIII deficiency NOS (D66)")
• Type 1 Excludes: D68.0 Von Willebrand disease ("factor VIII deficiency with functional defect (D66)")
• Code First: M36.2 Hemophilic arthropathy ("factor VIII deficiency (D66)")
• Code First: M36.2 Hemophilic arthropathy ("hemophilia (classical) (D66)")

Diagnosis Index entries for D66

• Arthritis, arthritic (acute) (chronic) (nonpyogenic) (subacute) › due to or associated with › hemophilia
• Arthritis, arthritic (acute) (chronic) (nonpyogenic) (subacute) › in (due to) › hemophilia NEC
• Arthropathy › hemophilic NEC
• Arthropathy › in (due to) › hemophilia NEC
• Deficiency, deficient › anti-hemophilic › factor (A)
• Deficiency, deficient › anti-hemophilic › globulin (AHG) NEC
• Deficiency, deficient › factor › VIII (congenital) (functional) (hereditary) (with functional defect)
• Disease, diseased › bleeder's
• Hemophilia (classical) (familial) (hereditary)
• Hemophilia (classical) (familial) (hereditary) › A
• Subhemophilia

Nearby codes

• D66 Hereditary factor VIII deficiency (this code)