D69.41 Evans syndrome
Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis.
Applies from D69 Purpura and other hemorrhagic conditions
Excludes1 (never code together)
- benign hypergammaglobulinemic purpura (D89.0)
- cryoglobulinemic purpura (D89.1)
- essential (hemorrhagic) thrombocythemia (D47.3)
- hemorrhagic thrombocythemia (D47.3)
- purpura fulminans (D65)
- thrombotic thrombocytopenic purpura (M31.19)
- Waldenström hypergammaglobulinemic purpura (D89.0)
Applies from D69.4 Other primary thrombocytopenia
Excludes1 (never code together)
- transient neonatal thrombocytopenia (P61.0)
- Wiskott-Aldrich syndrome (D82.0)
Risk adjustment (HCC)
- CMS-HCC V28: HCC 112 — Immune Thrombocytopenia and Specified Coagulation Defects and Hemorrhagic Conditions
- CMS-HCC V22: HCC 48 — Coagulation Defects and Other Specified Hematological Disorders
- ESRD V24: HCC 48
MS-DRG index
Defines the logic of DRG(s) 813 in MDC 16.
Approximate ICD-9-CM (GEMs)
Code annotations containing back-references to D69.41
Back-references to D69.41
- Type 2 Excludes:
D59.1 Other autoimmune hemolytic anemias ("Evans syndrome (D69.41)")
Back-references to D69
- Type 1 Excludes:
R23.3 Spontaneous ecchymoses ("purpura (D69.-)")
Diagnosis Index entries for D69.41
- Evans syndrome
- Syndrome › Evans
Nearby codes
D69.0 Allergic purpuraD69.1 Qualitative platelet defectsD69.2 Other nonthrombocytopenic purpuraD69.3 Immune thrombocytopenic purpuraD69.4 Other primary thrombocytopeniaD69.41 Evans syndrome (this code)D69.42 Congenital and hereditary thrombocytopenia purpuraD69.49 Other primary thrombocytopeniaD69.5 Secondary thrombocytopeniaD69.51 Posttransfusion purpuraD69.59 Other secondary thrombocytopenia