D74.0 Congenital methemoglobinemia

Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis.

Applicable to

• Congenital NADH-methemoglobin reductase deficiency
• Hemoglobin-M [Hb-M] disease
• Methemoglobinemia, hereditary

MS-DRG index

Defines the logic of DRG(s) 811-812 in MDC 16.

Approximate ICD-9-CM (GEMs)

• 289.7 Methemoglobinemia (approximate)

Code annotations containing back-references to D74.0

Back-references to D74.0

• Type 1 Excludes: D58.2 Other hemoglobinopathies ("Hb-M disease (D74.0)")

Back-references to D74

• Type 1 Excludes: D58.2 Other hemoglobinopathies ("methemoglobinemia (D74.-)")

Diagnosis Index entries for D74.0

• Deficiency, deficient › NADH diaphorase or reductase (congenital)
• Deficiency, deficient › NADH-methemoglobin reductase (congenital)
• Disease, diseased › diaphorase deficiency
• Disease, diseased › hemoglobin or Hb › M
• Methemoglobinemia › congenital
• Methemoglobinemia › enzymatic (congenital)
• Methemoglobinemia › Hb M disease
• Methemoglobinemia › hereditary

Nearby codes

• D74 Methemoglobinemia
• D74.0 Congenital methemoglobinemia (this code)
• D74.8 Other methemoglobinemias
• D74.9 Methemoglobinemia, unspecified