D76.3 Other histiocytosis syndromes
Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis.
Applicable to
- Reticulohistiocytoma (giant-cell)
- Sinus histiocytosis with massive lymphadenopathy
- Xanthogranuloma
Applies from D76 Other specified diseases with participation of lymphoreticular and reticulohistiocytic tissue
Excludes1 (never code together)
- (Abt-) Letterer-Siwe disease (C96.0)
- eosinophilic granuloma (C96.6)
- Hand-Schüller-Christian disease (C96.5)
- histiocytic medullary reticulosis (C96.9)
- histiocytic sarcoma (C96.A)
- histiocytosis X, multifocal (C96.5)
- histiocytosis X, unifocal (C96.6)
- Langerhans-cell histiocytosis, multifocal (C96.5)
- Langerhans-cell histiocytosis NOS (C96.6)
- Langerhans-cell histiocytosis, unifocal (C96.6)
- leukemic reticuloendotheliosis (C91.4-)
- lipomelanotic reticulosis (I89.8)
- malignant histiocytosis (C96.A)
- malignant reticulosis (C86.0)
- nonlipid reticuloendotheliosis (C96.0)
Risk adjustment (HCC)
- CMS-HCC V28: HCC 115 — Specified Immunodeficiencies and White Blood Cell Disorders
- CMS-HCC V22: HCC 47 — Disorders of Immunity
- ESRD V24: HCC 47
MS-DRG index
Defines the logic of DRG(s) 814-816 in MDC 16.
Approximate ICD-9-CM (GEMs)
288.4 Hemophagocytic syndromes (approximate)
Diagnosis Index entries for D76.3
- Granuloma › reticulohistiocytic
- Histiocytosis
- Histiocytosis › lipid, lipoid
- Histiocytosis › non-Langerhans cell
- Histiocytosis › polyostotic sclerosing
- Histiocytosis › sinus, with massive lymphadenopathy
- Histiocytosis › syndrome NEC
- Lipoid › histiocytosis
- Reticulohistiocytoma (giant-cell)
- Syndrome › histiocytic
- Syndrome › histiocytosis NEC
- Xanthogranuloma
Nearby codes
D76 Other specified diseases with participation of lymphoreticular and reticulohistiocytic tissueD76.1 Hemophagocytic lymphohistiocytosisD76.2 Hemophagocytic syndrome, infection-associatedD76.3 Other histiocytosis syndromes (this code)