`E31.0` Autoimmune polyglandular failure

Billable ICD-10-CM code, FY2026.

Applicable to

Schmidt's syndrome

Applies from E31 Polyglandular dysfunction

Excludes1 (never code together)

ataxia telangiectasia [Louis-Bar] (G11.3)
dystrophia myotonica [Steinert] (G71.11)
pseudohypoparathyroidism (E20.1)

Risk adjustment (HCC)

CMS-HCC V28: HCC 51 — Addison's and Cushing's Diseases, Acromegaly, and Other Specified Endocrine Disorders
CMS-HCC V22: HCC 23 — Other Significant Endocrine and Metabolic Disorders
RxHCC V08: HCC 43 — Pituitary, Adrenal Gland, and Other Endocrine and Metabolic Disorders
ESRD V24: HCC 23

MS-DRG index

Defines the logic of DRG(s) 643-645 in MDC 10.

Approximate ICD-9-CM (GEMs)

258.1 Other combinations of endocrine dysfunction (approximate)

Code annotations containing back-references to E31.0

Back-references to E31.0

Code First: E20.812 Autoimmune hypoparathyroidism ("autoimmune polyglandular failure (E31.0)")
Code First: E20.812 Autoimmune hypoparathyroidism ("Schmidt's syndrome (E31.0)")

Back-references to E31

Code First: G63 Polyneuropathy in diseases classified elsewhere ("endocrine disease, except diabetes (E00-E07, E15-E16, E20-E34)")

Diagnosis Index entries for E31.0

Atrophy, atrophic (of) › pluriglandular › autoimmune
Deficiency, deficient › polyglandular › autoimmune
Failure, failed › polyglandular, autoimmune
Insufficiency, insufficient › progressive pluriglandular
Polyglandular › deficiency
Schmidt's syndrome (polyglandular, autoimmune)
Syndrome › autoimmune polyglandular
Syndrome › pluriglandular (compensatory) › autoimmune
Syndrome › polyglandular › autoimmune
Syndrome › thyroid-adrenocortical insufficiency

Nearby codes

E31 Polyglandular dysfunction
E31.0 Autoimmune polyglandular failure (this code)
E31.1 Polyglandular hyperfunction
E31.2 Multiple endocrine neoplasia [MEN] syndromes
E31.20 Multiple endocrine neoplasia [MEN] syndrome, unspecified
E31.21 Multiple endocrine neoplasia [MEN] type I
E31.22 Multiple endocrine neoplasia [MEN] type IIA