E71.3 Disorders of fatty-acid metabolism

Non-billable header with 4 child codes.

Excludes1 (never code together)

• peroxisomal disorders (E71.5)
• Refsum's disease (G60.1)
• Schilder's disease (G37.0)

Excludes2 (not included here)

• carnitine deficiency due to inborn error of metabolism (E71.42)

Codes under E71.3

• E71.30 Disorder of fatty-acid metabolism, unspecified
• E71.31 Disorders of fatty-acid oxidation
• E71.32 Disorders of ketone metabolism
• E71.39 Other disorders of fatty-acid metabolism

Code annotations containing back-references to E71.3

Back-references to E71.3

• Type 1 Excludes: E72 Other disorders of amino-acid metabolism ("fatty-acid metabolism (E71.3)")

Back-references to E71

• Type 2 Excludes: G11 Hereditary ataxia ("metabolic disorders (E70-E88)")
• Code First: G63 Polyneuropathy in diseases classified elsewhere ("metabolic diseases (E70-E88)")
• Type 2 Excludes: G71 Primary disorders of muscles ("metabolic disorders (E70-E88)")
• Code First: H42 Glaucoma in diseases classified elsewhere ("specified metabolic disorder (E70-E88)")
• Type 2 Excludes: N25.0 Renal osteodystrophy ("metabolic disorders classifiable to E70-E88")
• Type 2 Excludes: N25.81 Secondary hyperparathyroidism of renal origin ("metabolic disorders classifiable to E70-E88")
• Type 1 Excludes: P59 Neonatal jaundice from other and unspecified causes ("jaundice due to inborn errors of metabolism (E70-E88)")
• Type 1 Excludes: R79 Other abnormal findings of blood chemistry ("specific findings indicating disorder of amino-acid metabolism (E70-E72)")
• Type 1 Excludes: R79.83 Abnormal findings of blood amino-acid level ("disorders of amino-acid metabolism (E70-E72)")

Nearby codes

• E71.120 Methylmalonic acidemia
• E71.121 Propionic acidemia
• E71.128 Other disorders of propionate metabolism
• E71.19 Other disorders of branched-chain amino-acid metabolism
• E71.2 Disorder of branched-chain amino-acid metabolism, unspecified
• E71.3 Disorders of fatty-acid metabolism (this code)
• E71.30 Disorder of fatty-acid metabolism, unspecified
• E71.31 Disorders of fatty-acid oxidation
• E71.310 Long chain/very long chain acyl CoA dehydrogenase deficiency
• E71.311 Medium chain acyl CoA dehydrogenase deficiency
• E71.312 Short chain acyl CoA dehydrogenase deficiency