E72.53 Primary hyperoxaluria

Non-billable header with 3 child codes.

Applicable to

• Oxalosis
• Oxaluria

Excludes1 (never code together)

• secondary hyperoxaluria (E72.54-)

Applies from E72 Other disorders of amino-acid metabolism

Excludes1 (never code together)

• disorders of:
• aromatic amino-acid metabolism (E70.-)
• branched-chain amino-acid metabolism (E71.0-E71.2)
• fatty-acid metabolism (E71.3)
• purine and pyrimidine metabolism (E79.-)
• gout (M1A.-, M10.-)

Codes under E72.53

• E72.530 Primary hyperoxaluria, type 1
• E72.538 Other specified primary hyperoxaluria
• E72.539 Primary hyperoxaluria, unspecified

Risk adjustment (HCC)

• CMS-HCC V28: HCC 50 — Amyloidosis, Porphyria, and Other Specified Metabolic Disorders
• CMS-HCC V22: HCC 23 — Other Significant Endocrine and Metabolic Disorders
• RxHCC V08: HCC 43 — Pituitary, Adrenal Gland, and Other Endocrine and Metabolic Disorders
• ESRD V24: HCC 23

Approximate ICD-9-CM (GEMs)

• 271.8 Other specified disorders of carbohydrate transport and metabolism (approximate)

Code annotations containing back-references to E72.53

Back-references to E72.53

• Type 1 Excludes: E72.54 Secondary hyperoxaluria ("primary hyperoxaluria (E72.53-)")
• Type 1 Excludes: R82.992 Hyperoxaluria ("primary hyperoxaluria (E72.53-)")

Back-references to E72

• Type 2 Excludes: G11 Hereditary ataxia ("metabolic disorders (E70-E88)")
• Code First: G63 Polyneuropathy in diseases classified elsewhere ("metabolic diseases (E70-E88)")
• Type 2 Excludes: G71 Primary disorders of muscles ("metabolic disorders (E70-E88)")
• Code First: H42 Glaucoma in diseases classified elsewhere ("specified metabolic disorder (E70-E88)")
• Type 2 Excludes: N25.0 Renal osteodystrophy ("metabolic disorders classifiable to E70-E88")
• Type 2 Excludes: N25.81 Secondary hyperparathyroidism of renal origin ("metabolic disorders classifiable to E70-E88")
• Type 1 Excludes: P59 Neonatal jaundice from other and unspecified causes ("jaundice due to inborn errors of metabolism (E70-E88)")
• Type 1 Excludes: R79 Other abnormal findings of blood chemistry ("specific findings indicating disorder of amino-acid metabolism (E70-E72)")
• Type 1 Excludes: R79.83 Abnormal findings of blood amino-acid level ("disorders of amino-acid metabolism (E70-E72)")

Diagnosis Index entries for E72.53

• Disorder (of) › glycine metabolism › oxalosis
• Disorder (of) › glycine metabolism › oxaluria
• Disorder (of) › metabolism NOS › amino-acid › glycine › hyperoxaluria › primary
• Hyperoxaluria › primary
• Oxalosis
• Oxaluria

Nearby codes

• E72.4 Disorders of ornithine metabolism
• E72.5 Disorders of glycine metabolism
• E72.50 Disorder of glycine metabolism, unspecified
• E72.51 Non-ketotic hyperglycinemia
• E72.52 Trimethylaminuria
• E72.53 Primary hyperoxaluria (this code)
• E72.530 Primary hyperoxaluria, type 1
• E72.538 Other specified primary hyperoxaluria
• E72.539 Primary hyperoxaluria, unspecified
• E72.54 Secondary hyperoxaluria
• E72.540 Dietary hyperoxaluria