E74.89 Other specified disorders of carbohydrate metabolism

Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis.

Applicable to

• Essential pentosuria

Applies from E74 Other disorders of carbohydrate metabolism

Excludes1 (never code together)

• diabetes mellitus (E08-E13)
• hypoglycemia NOS (E16.2)
• increased secretion of glucagon (E16.3)
• mucopolysaccharidosis (E76.0-E76.3)

Risk adjustment (HCC)

• CMS-HCC V22: HCC 23 — Other Significant Endocrine and Metabolic Disorders
• RxHCC V08: HCC 43 — Pituitary, Adrenal Gland, and Other Endocrine and Metabolic Disorders
• ESRD V24: HCC 23

MS-DRG index

Defines the logic of DRG(s) 642 in MDC 10.

Code annotations containing back-references to E74.89

Back-references to E74

• Type 2 Excludes: G11 Hereditary ataxia ("metabolic disorders (E70-E88)")
• Code First: G63 Polyneuropathy in diseases classified elsewhere ("metabolic diseases (E70-E88)")
• Type 2 Excludes: G71 Primary disorders of muscles ("metabolic disorders (E70-E88)")
• Code First: H42 Glaucoma in diseases classified elsewhere ("specified metabolic disorder (E70-E88)")
• Type 2 Excludes: N25.0 Renal osteodystrophy ("metabolic disorders classifiable to E70-E88")
• Type 2 Excludes: N25.81 Secondary hyperparathyroidism of renal origin ("metabolic disorders classifiable to E70-E88")
• Type 1 Excludes: P59 Neonatal jaundice from other and unspecified causes ("jaundice due to inborn errors of metabolism (E70-E88)")
• Type 1 Excludes: R79 Other abnormal findings of blood chemistry ("specific findings indicating disorder of carbohydrate metabolism (E73-E74)")

Diagnosis Index entries for E74.89

• Disorder (of) › carbohydrate › metabolism (congenital) › specified NEC
• Disorder (of) › congenital glycosylation (CDG)
• Disorder (of) › metabolism NOS › carbohydrate › specified NEC
• Pentosuria (essential)

Nearby codes

• E74.818 Other disorders of glucose transport
• E74.819 Disorders of glucose transport, unspecified
• E74.82 Disorders of citrate metabolism
• E74.820 SLC13A5 Citrate Transporter Disorder
• E74.829 Other disorders of citrate metabolism
• E74.89 Other specified disorders of carbohydrate metabolism (this code)
• E74.9 Disorder of carbohydrate metabolism, unspecified