E75.00 GM2 gangliosidosis, unspecifiedBillable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis.
Defines the logic of DRG(s) 056-057 in MDC 01.
330.1 Cerebral lipidoses (approximate)E78 Disorders of lipoprotein metabolism and other lipidemias ("sphingolipidosis (E75.0-E75.3)")G11 Hereditary ataxia ("metabolic disorders (E70-E88)")G63 Polyneuropathy in diseases classified elsewhere ("metabolic diseases (E70-E88)")G71 Primary disorders of muscles ("metabolic disorders (E70-E88)")G73.7 Myopathy in diseases classified elsewhere ("lipid storage disorders (E75.-)")H36 Retinal disorders in diseases classified elsewhere ("lipid storage disorders (E75.-)")H42 Glaucoma in diseases classified elsewhere ("specified metabolic disorder (E70-E88)")N25.0 Renal osteodystrophy ("metabolic disorders classifiable to E70-E88")N25.81 Secondary hyperparathyroidism of renal origin ("metabolic disorders classifiable to E70-E88")P59 Neonatal jaundice from other and unspecified causes ("jaundice due to inborn errors of metabolism (E70-E88)")R79 Other abnormal findings of blood chemistry ("specific findings indicating disorder of lipid metabolism (E75.-)")E75 Disorders of sphingolipid metabolism and other lipid storage disordersE75.0 GM2 gangliosidosisE75.00 GM2 gangliosidosis, unspecified (this code)E75.01 Sandhoff diseaseE75.02 Tay-Sachs diseaseE75.09 Other GM2 gangliosidosisE75.1 Other and unspecified gangliosidosisE75.10 Unspecified gangliosidosis