E76.0 Mucopolysaccharidosis, type I

Non-billable header with 3 child codes.

Codes under E76.0

• E76.01 Hurler's syndrome
• E76.02 Hurler-Scheie syndrome
• E76.03 Scheie's syndrome

Code annotations containing back-references to E76.0

Back-references to E76.0

• Type 1 Excludes: E74 Other disorders of carbohydrate metabolism ("mucopolysaccharidosis (E76.0-E76.3)")
• Type 1 Excludes: Q77 Osteochondrodysplasia with defects of growth of tubular bones and spine ("mucopolysaccharidosis (E76.0-E76.3)")

Back-references to E76

• Type 2 Excludes: G11 Hereditary ataxia ("metabolic disorders (E70-E88)")
• Code First: G63 Polyneuropathy in diseases classified elsewhere ("metabolic diseases (E70-E88)")
• Type 2 Excludes: G71 Primary disorders of muscles ("metabolic disorders (E70-E88)")
• Code First: H42 Glaucoma in diseases classified elsewhere ("specified metabolic disorder (E70-E88)")
• Type 2 Excludes: N25.0 Renal osteodystrophy ("metabolic disorders classifiable to E70-E88")
• Type 2 Excludes: N25.81 Secondary hyperparathyroidism of renal origin ("metabolic disorders classifiable to E70-E88")
• Type 1 Excludes: P59 Neonatal jaundice from other and unspecified causes ("jaundice due to inborn errors of metabolism (E70-E88)")

Nearby codes

• E76 Disorders of glycosaminoglycan metabolism
• E76.0 Mucopolysaccharidosis, type I (this code)
• E76.01 Hurler's syndrome
• E76.02 Hurler-Scheie syndrome
• E76.03 Scheie's syndrome
• E76.1 Mucopolysaccharidosis, type II
• E76.2 Other mucopolysaccharidoses