E83.31 Familial hypophosphatemia

Billable ICD-10-CM code, FY2026.

Applicable to

• Vitamin D-resistant osteomalacia
• Vitamin D-resistant rickets

Excludes1 (never code together)

• vitamin D-deficiency rickets (E55.0)

Applies from E83 Disorders of mineral metabolism

Excludes1 (never code together)

• dietary mineral deficiency (E58-E61)
• parathyroid disorders (E20-E21)
• vitamin D deficiency (E55.-)

Applies from E83.3 Disorders of phosphorus metabolism and phosphatases

Excludes1 (never code together)

• adult osteomalacia (M83.-)
• osteoporosis (M80.-)

Excludes2 (not included here)

• disorders of pyrophosphate metabolism (E83.82-)

Risk adjustment (HCC)

• CMS-HCC V28: HCC 50 — Amyloidosis, Porphyria, and Other Specified Metabolic Disorders
• RxHCC V08: HCC 42 — Acromegaly and Other Endocrine and Metabolic Disorders

MS-DRG index

Defines the logic of DRG(s) 642 in MDC 10.

Approximate ICD-9-CM (GEMs)

• 275.3 Disorders of phosphorus metabolism (approximate)

Code annotations containing back-references to E83.31

Back-references to E83.31

• Type 1 Excludes: E55.0 Rickets, active ("vitamin D-resistant rickets (E83.31)")
• Type 1 Excludes: M83 Adult osteomalacia ("vitamin D-resistant osteomalacia (E83.31)")
• Type 1 Excludes: M83 Adult osteomalacia ("vitamin D-resistant rickets (active) (E83.31)")
• Code First: M90.8 Osteopathy in diseases classified elsewhere ("vitamin-D-resistant rickets (E83.31)")

Back-references to E83

• Type 1 Excludes: E61 Deficiency of other nutrient elements ("disorders of mineral metabolism (E83.-)")
• Type 2 Excludes: G11 Hereditary ataxia ("metabolic disorders (E70-E88)")
• Code First: G63 Polyneuropathy in diseases classified elsewhere ("metabolic diseases (E70-E88)")
• Type 2 Excludes: G71 Primary disorders of muscles ("metabolic disorders (E70-E88)")
• Code First: H42 Glaucoma in diseases classified elsewhere ("specified metabolic disorder (E70-E88)")
• Type 2 Excludes: N25.0 Renal osteodystrophy ("metabolic disorders classifiable to E70-E88")
• Type 2 Excludes: N25.81 Secondary hyperparathyroidism of renal origin ("metabolic disorders classifiable to E70-E88")
• Type 1 Excludes: P59 Neonatal jaundice from other and unspecified causes ("jaundice due to inborn errors of metabolism (E70-E88)")
• Type 1 Excludes: R79.0 Abnormal level of blood mineral ("disorders of mineral metabolism (E83.-)")

Diagnosis Index entries for E83.31

• Disorder (of) › metabolism NOS › phosphorus › hypophosphatemia › familial
• Hypophosphatemia, hypophosphatasia (acquired) (congenital) (renal) › familial
• Osteomalacia › vitamin-D-resistant in adults
• Osteomalacia › vitamin-D-resistant in adults › carpus
• Osteomalacia › vitamin-D-resistant in adults › clavicle
• Osteomalacia › vitamin-D-resistant in adults › femur
• Osteomalacia › vitamin-D-resistant in adults › fibula
• Osteomalacia › vitamin-D-resistant in adults › finger
• Osteomalacia › vitamin-D-resistant in adults › humerus
• Osteomalacia › vitamin-D-resistant in adults › ilium
• Osteomalacia › vitamin-D-resistant in adults › ischium
• Osteomalacia › vitamin-D-resistant in adults › metacarpus
• Osteomalacia › vitamin-D-resistant in adults › metatarsus
• Osteomalacia › vitamin-D-resistant in adults › multiple sites
• Osteomalacia › vitamin-D-resistant in adults › neck
• Osteomalacia › vitamin-D-resistant in adults › radius
• Osteomalacia › vitamin-D-resistant in adults › rib
• Osteomalacia › vitamin-D-resistant in adults › scapula
• Osteomalacia › vitamin-D-resistant in adults › skull
• Osteomalacia › vitamin-D-resistant in adults › tarsus
• Osteomalacia › vitamin-D-resistant in adults › tibia
• Osteomalacia › vitamin-D-resistant in adults › toe
• Osteomalacia › vitamin-D-resistant in adults › ulna
• Osteomalacia › vitamin-D-resistant in adults › vertebra
• Rickets (active) (acute) (adolescent) (chest wall) (congenital) (current) (infantile) (intestinal) › vitamin-D-resistant

Nearby codes

• E83.119 Hemochromatosis, unspecified
• E83.19 Other disorders of iron metabolism
• E83.2 Disorders of zinc metabolism
• E83.3 Disorders of phosphorus metabolism and phosphatases
• E83.30 Disorder of phosphorus metabolism, unspecified
• E83.31 Familial hypophosphatemia (this code)
• E83.32 Hereditary vitamin D-dependent rickets (type 1) (type 2)
• E83.39 Other disorders of phosphorus metabolism
• E83.4 Disorders of magnesium metabolism
• E83.40 Disorders of magnesium metabolism, unspecified
• E83.41 Hypermagnesemia