G71.033 Limb girdle muscular dystrophy due to dysferlin dysfunction

Billable ICD-10-CM code, FY2026.

Applicable to

• Dysferlinopathy
• LGMD R2 dysferlin-related
• Limb girdle muscular dystrophy type 2B
• Miyoshi Myopathy type 1

Applies from G71 Primary disorders of muscles

Excludes2 (not included here)

• arthrogryposis multiplex congenita (Q74.3)
• metabolic disorders (E70-E88)
• myositis (M60.-)

Risk adjustment (HCC)

• CMS-HCC V28: HCC 197 — Muscular Dystrophy
• CMS-HCC V22: HCC 76 — Muscular Dystrophy
• ESRD V24: HCC 76

MS-DRG index

Defines the logic of DRG(s) 091-093 in MDC 01.

Code annotations containing back-references to G71.033

Back-references to G71.0

• Code First: Z99.3 Dependence on wheelchair ("muscular dystrophy (G71.0-)")

Back-references to G71

• Code First: M62.84 Sarcopenia ("primary disorders of muscles (G71.-)")

Diagnosis Index entries for G71.033

• Dysferlinopathy
• Dystrophy, dystrophia › muscular › limb-girdle › R2 (autosomal recessive)
• Dystrophy, dystrophia › muscular › limb-girdle › type 2B (autosomal recessive)

Nearby codes

• G71.01 Duchenne or Becker muscular dystrophy
• G71.02 Facioscapulohumeral muscular dystrophy
• G71.03 Limb girdle muscular dystrophies
• G71.031 Autosomal dominant limb girdle muscular dystrophy
• G71.032 Autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction
• G71.033 Limb girdle muscular dystrophy due to dysferlin dysfunction (this code)
• G71.034 Limb girdle muscular dystrophy due to sarcoglycan dysfunction
• G71.0340 Limb girdle muscular dystrophy due to sarcoglycan dysfunction, unspecified
• G71.0341 Limb girdle muscular dystrophy due to alpha sarcoglycan dysfunction
• G71.0342 Limb girdle muscular dystrophy due to beta sarcoglycan dysfunction
• G71.0349 Limb girdle muscular dystrophy due to other sarcoglycan dysfunction