G71.0342 Limb girdle muscular dystrophy due to beta sarcoglycan dysfunction

Billable ICD-10-CM code, FY2026.

Applicable to

• Beta sarcoglycanopathy
• Limb girdle muscular dystrophy due to beta-sarcoglycan deficiency
• Limb girdle muscular dystrophy type 2E

Applies from G71 Primary disorders of muscles

Excludes2 (not included here)

• arthrogryposis multiplex congenita (Q74.3)
• metabolic disorders (E70-E88)
• myositis (M60.-)

Risk adjustment (HCC)

• CMS-HCC V28: HCC 197 — Muscular Dystrophy
• CMS-HCC V22: HCC 76 — Muscular Dystrophy
• ESRD V24: HCC 76

MS-DRG index

Defines the logic of DRG(s) 091-093 in MDC 01.

Code annotations containing back-references to G71.0342

Back-references to G71.0

• Code First: Z99.3 Dependence on wheelchair ("muscular dystrophy (G71.0-)")

Back-references to G71

• Code First: M62.84 Sarcopenia ("primary disorders of muscles (G71.-)")

Diagnosis Index entries for G71.0342

• Dystrophy, dystrophia › muscular › limb-girdle › beta-sarcoglycan-related
• Dystrophy, dystrophia › muscular › limb-girdle › due to › beta sarcoglycan dysfunction
• Dystrophy, dystrophia › muscular › limb-girdle › R4 (autosomal recessive)
• Dystrophy, dystrophia › muscular › limb-girdle › type 2E (autosomal recessive)
• Sarcoglycanopathy › beta

Nearby codes

• G71.032 Autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction
• G71.033 Limb girdle muscular dystrophy due to dysferlin dysfunction
• G71.034 Limb girdle muscular dystrophy due to sarcoglycan dysfunction
• G71.0340 Limb girdle muscular dystrophy due to sarcoglycan dysfunction, unspecified
• G71.0341 Limb girdle muscular dystrophy due to alpha sarcoglycan dysfunction
• G71.0342 Limb girdle muscular dystrophy due to beta sarcoglycan dysfunction (this code)
• G71.0349 Limb girdle muscular dystrophy due to other sarcoglycan dysfunction
• G71.035 Limb girdle muscular dystrophy due to anoctamin-5 dysfunction
• G71.036 Limb girdle muscular dystrophy due to fukutin related protein dysfunction
• G71.038 Other limb girdle muscular dystrophy
• G71.039 Limb girdle muscular dystrophy, unspecified