H47.22 Hereditary optic atrophy

Billable ICD-10-CM code, FY2026.

Applicable to

• Leber's optic atrophy

MS-DRG index

Defines the logic of DRG(s) 123 in MDC 02.

Approximate ICD-9-CM (GEMs)

• 377.16 Hereditary optic atrophy

Code annotations containing back-references to H47.22

Back-references to H47.22

• Type 1 Excludes: E88.4 Mitochondrial metabolism disorders ("Leber's disease (H47.22)")

Diagnosis Index entries for H47.22

• Atrophy, atrophic (of) › Leber's optic (hereditary)
• Atrophy, atrophic (of) › optic (nerve) › hereditary
• Leber's › optic atrophy (hereditary)
• Neuroretinopathy, hereditary optic

Nearby codes

• H47.21 Primary optic atrophy
• H47.211 Primary optic atrophy, right eye
• H47.212 Primary optic atrophy, left eye
• H47.213 Primary optic atrophy, bilateral
• H47.219 Primary optic atrophy, unspecified eye
• H47.22 Hereditary optic atrophy (this code)
• H47.23 Glaucomatous optic atrophy
• H47.231 Glaucomatous optic atrophy, right eye
• H47.232 Glaucomatous optic atrophy, left eye
• H47.233 Glaucomatous optic atrophy, bilateral
• H47.239 Glaucomatous optic atrophy, unspecified eye