H49.81 Kearns-Sayre syndrome

Non-billable header with 4 child codes.

Applicable to

• Progressive external ophthalmoplegia with pigmentary retinopathy

Code also

• , if applicable, other manifestations, such as:
• heart block (I45.9)

Applies from H49 Paralytic strabismus

Excludes2 (not included here)

• internal ophthalmoplegia (H52.51-)
• internuclear ophthalmoplegia (H51.2-)
• progressive supranuclear ophthalmoplegia (G23.1)

Codes under H49.81

• H49.811 Kearns-Sayre syndrome, right eye
• H49.812 Kearns-Sayre syndrome, left eye
• H49.813 Kearns-Sayre syndrome, bilateral
• H49.819 Kearns-Sayre syndrome, unspecified eye

Code annotations containing back-references to H49.81

Back-references to H49.81

• Type 1 Excludes: E88.4 Mitochondrial metabolism disorders ("Kearns-Sayre syndrome (H49.81)")
• Type 1 Excludes: G71.3 Mitochondrial myopathy, not elsewhere classified ("Kearns-Sayre syndrome (H49.81)")
• Type 1 Excludes: H49.4 Progressive external ophthalmoplegia ("Kearns-Sayre syndrome (H49.81-)")

Diagnosis Index entries for H49.81

• Kearns-Sayre syndrome
• Strabismus (congenital) (nonparalytic) › paralytic › Kearns-Sayre syndrome
• Strabismus (congenital) (nonparalytic) › paralytic › ophthalmoplegia (external) › progressive › with pigmentary retinopathy

Nearby codes

• H49.40 Progressive external ophthalmoplegia, unspecified eye
• H49.41 Progressive external ophthalmoplegia, right eye
• H49.42 Progressive external ophthalmoplegia, left eye
• H49.43 Progressive external ophthalmoplegia, bilateral
• H49.8 Other paralytic strabismus
• H49.81 Kearns-Sayre syndrome (this code)
• H49.811 Kearns-Sayre syndrome, right eye
• H49.812 Kearns-Sayre syndrome, left eye
• H49.813 Kearns-Sayre syndrome, bilateral
• H49.819 Kearns-Sayre syndrome, unspecified eye
• H49.88 Other paralytic strabismus