I01.1 Acute rheumatic endocarditis

Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis.

Applicable to

• Any condition in I00 with endocarditis or valvulitis
• Acute rheumatic valvulitis

Applies from I01 Rheumatic fever with heart involvement

Excludes1 (never code together)

• chronic diseases of rheumatic origin (I05-I09) unless rheumatic fever is also present or there is evidence of reactivation or activity of the rheumatic process.

MS-DRG index

Defines the logic of DRG(s) 306-307 in MDC 05.

Approximate ICD-9-CM (GEMs)

• 391.1 Acute rheumatic endocarditis

Code annotations containing back-references to I01.1

Back-references to I01.1

• Type 1 Excludes: I00 Rheumatic fever without heart involvement ("rheumatic fever with heart involvement (I01.0 -I01.9)")
• Type 1 Excludes: I33 Acute and subacute endocarditis ("acute rheumatic endocarditis (I01.1)")

Back-references to I01

• Type 2 Excludes: I51 Complications and ill-defined descriptions of heart disease ("heart disease specified as rheumatic (I00-I09)")

Diagnosis Index entries for I01.1

• Endocarditis (chronic) (marantic) (nonbacterial) (thrombotic) (valvular) › acute or subacute › rheumatic (aortic) (mitral) (pulmonary) (tricuspid)
• Endocarditis (chronic) (marantic) (nonbacterial) (thrombotic) (valvular) › aortic (heart) (nonrheumatic) (valve) › with › mitral disease › active or acute
• Endocarditis (chronic) (marantic) (nonbacterial) (thrombotic) (valvular) › aortic (heart) (nonrheumatic) (valve) › rheumatic › with mitral disease › active or acute
• Endocarditis (chronic) (marantic) (nonbacterial) (thrombotic) (valvular) › aortic (heart) (nonrheumatic) (valve) › rheumatic › active or acute
• Endocarditis (chronic) (marantic) (nonbacterial) (thrombotic) (valvular) › mitral (chronic) (double) (fibroid) (heart) (inactive) (valve) (with chorea) › with › aortic (valve) disease › active or acute
• Endocarditis (chronic) (marantic) (nonbacterial) (thrombotic) (valvular) › mitral (chronic) (double) (fibroid) (heart) (inactive) (valve) (with chorea) › active or acute
• Endocarditis (chronic) (marantic) (nonbacterial) (thrombotic) (valvular) › pulmonary (chronic) (heart) (valve) › acute or subacute › rheumatic
• Endocarditis (chronic) (marantic) (nonbacterial) (thrombotic) (valvular) › pulmonary (chronic) (heart) (valve) › rheumatic (chronic) (inactive) (with chorea) › active or acute
• Endocarditis (chronic) (marantic) (nonbacterial) (thrombotic) (valvular) › rheumatic (chronic) (inactive) (with chorea) › active or acute (aortic) (mitral) (pulmonary) (tricuspid)
• Endocarditis (chronic) (marantic) (nonbacterial) (thrombotic) (valvular) › tricuspid (chronic) (heart) (inactive) (rheumatic) (valve) (with chorea) › active or acute
• Insufficiency, insufficient › mitral (valve) › rheumatic › active or acute
• Stenosis, stenotic (cicatricial) › mitral (chronic) (inactive) (valve) › active or acute

Nearby codes

• I01 Rheumatic fever with heart involvement
• I01.0 Acute rheumatic pericarditis
• I01.1 Acute rheumatic endocarditis (this code)
• I01.2 Acute rheumatic myocarditis
• I01.8 Other acute rheumatic heart disease
• I01.9 Acute rheumatic heart disease, unspecified