I01.9 Acute rheumatic heart disease, unspecified

Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis.

Applicable to

• Any condition in I00 with unspecified type of heart involvement
• Rheumatic carditis, acute
• Rheumatic heart disease, active or acute

Applies from I01 Rheumatic fever with heart involvement

Excludes1 (never code together)

• chronic diseases of rheumatic origin (I05-I09) unless rheumatic fever is also present or there is evidence of reactivation or activity of the rheumatic process.

MS-DRG index

Defines the logic of DRG(s) 314-316 in MDC 05.

Approximate ICD-9-CM (GEMs)

• 391.9 Acute rheumatic heart disease, unspecified

Code annotations containing back-references to I01.9

Back-references to I01.9

• Type 1 Excludes: I00 Rheumatic fever without heart involvement ("rheumatic fever with heart involvement (I01.0 -I01.9)")

Back-references to I01

• Type 2 Excludes: I51 Complications and ill-defined descriptions of heart disease ("heart disease specified as rheumatic (I00-I09)")

Diagnosis Index entries for I01.9

• Bouillaud's disease or syndrome (rheumatic heart disease)
• Disease, diseased › Bouillaud's (rheumatic heart disease)
• Disease, diseased › heart (organic) › with › rheumatic fever (conditions in I00) › active
• Disease, diseased › heart (organic) › rheumatic (chronic) (inactive) (old) (quiescent) (with chorea) › active or acute
• Syndrome › Bouillaud's

Nearby codes

• I01 Rheumatic fever with heart involvement
• I01.0 Acute rheumatic pericarditis
• I01.1 Acute rheumatic endocarditis
• I01.2 Acute rheumatic myocarditis
• I01.8 Other acute rheumatic heart disease
• I01.9 Acute rheumatic heart disease, unspecified (this code)