Billable ICD-10-CM code, FY2026. Acts as a Major Complication or Comorbidity (MCC) as a secondary diagnosis.
Excludes1 (never code together)
myocarditis (in):
Chagas' disease (chronic) (B57.2)
acute (B57.0)
coxsackie (virus) infection (B33.22)
diphtheritic (A36.81)
gonococcal (A54.83)
influenzal (J09.X9, J10.82, J11.82)
meningococcal (A39.52)
mumps (B26.82)
rheumatoid arthritis (M05.31)
sarcoid (D86.85)
syphilis (A52.06)
toxoplasmosis (B58.81)
tuberculous (A18.84)
Code first
underlying disease, such as:
typhus (A75.0-A75.9)
Applies from I41 Myocarditis in diseases classified elsewhere
Excludes1 (never code together)
myocarditis (in):
Chagas' disease (chronic) (B57.2)
acute (B57.0)
coxsackie (virus) infection (B33.22)
diphtheritic (A36.81)
gonococcal (A54.83)
influenzal (J09.X9, J10.82, J11.82)
meningococcal (A39.52)
mumps (B26.82)
rheumatoid arthritis (M05.31)
sarcoid (D86.85)
syphilis (A52.06)
toxoplasmosis (B58.81)
tuberculous (A18.84)
Code first
underlying disease, such as:
typhus (A75.0-A75.9)
MS-DRG index
Defines the logic of DRG(s) 314-316 in MDC 05.
Approximate ICD-9-CM (GEMs)
422.0 Acute myocarditis in diseases classified elsewhere (approximate)
Medicare Code Edits (MCE v43.1 (April 2026))
Manifestation codes as principal diagnosis: Manifestation codes describe the manifestation of an underlying disease, not the disease itself, and are not allowed as principal diagnosis.