I67.5 Moyamoya disease

Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis.

Applies from I67 Other cerebrovascular diseases

Excludes1 (never code together)

• Occlusion and stenosis of cerebral artery causing cerebral infarction (I63.3-I63.5-)
• Occlusion and stenosis of precerebral artery causing cerebral infarction (I63.2-)

Excludes2 (not included here)

• sequelae of the listed conditions (I69.8)

MS-DRG index

Defines the logic of DRG(s) 091-093 in MDC 01.

Approximate ICD-9-CM (GEMs)

• 437.5 Moyamoya disease

Code annotations containing back-references to I67.5

Back-references to I67

• Type 1 Excludes: G31.84 Mild cognitive impairment of uncertain or unknown etiology ("cerebrovascular diseases (I60-I69)")
• Code First: G46 Vascular syndromes of brain in cerebrovascular diseases ("underlying cerebrovascular disease (I60-I69)")
• Type 2 Excludes: I10 Essential (primary) hypertension ("essential (primary) hypertension involving vessels of brain (I60-I69)")
• Type 2 Excludes: I15 Secondary hypertension ("secondary hypertension involving vessels of brain (I60-I69)")

Diagnosis Index entries for I67.5

• Disease, diseased › moyamoya
• Disease, diseased › Nishimoto (-Takeuchi)
• Encephaloduroarteriomyosynangiosis (EDAMS)
• Moyamoya disease
• Nishimoto (-Takeuchi) disease

Nearby codes

• I67.0 Dissection of cerebral arteries, nonruptured
• I67.1 Cerebral aneurysm, nonruptured
• I67.2 Cerebral atherosclerosis
• I67.3 Progressive vascular leukoencephalopathy
• I67.4 Hypertensive encephalopathy
• I67.5 Moyamoya disease (this code)
• I67.6 Nonpyogenic thrombosis of intracranial venous system
• I67.7 Cerebral arteritis, not elsewhere classified
• I67.8 Other specified cerebrovascular diseases
• I67.81 Acute cerebrovascular insufficiency
• I67.82 Cerebral ischemia