J84.112 Idiopathic pulmonary fibrosis
Billable ICD-10-CM code, FY2026.
Applicable to
- Cryptogenic fibrosing alveolitis
- Idiopathic fibrosing alveolitis
Applies from J84 Other interstitial pulmonary diseases
Excludes1 (never code together)
- drug-induced interstitial lung disorders (J70.2-J70.4)
- interstitial emphysema (J98.2)
Excludes2 (not included here)
- lung diseases due to external agents (J60-J70)
Code also
- , if applicable, associated condition
Applies from J84.1 Other interstitial pulmonary diseases with fibrosis
Excludes1 (never code together)
- pulmonary fibrosis (chronic) following radiation (J70.1)
Code also
- , if applicable, pulmonary fibrosis (chronic) due to inhalation of chemicals, gases, fumes or vapors (J68.4)
Applies from J84.11 Idiopathic interstitial pneumonia
Excludes1 (never code together)
- lymphoid interstitial pneumonia (J84.2)
- pneumocystis pneumonia (B59)
Risk adjustment (HCC)
- CMS-HCC V28: HCC 278 — Idiopathic Pulmonary Fibrosis and Lung Involvement in Systemic Sclerosis
- CMS-HCC V22: HCC 112 — Fibrosis of Lung and Other Chronic Lung Disorders
- RxHCC V08: HCC 226 — Idiopathic Pulmonary Fibrosis and Systemic Sclerosis with Lung Involvement
- ESRD V24: HCC 112
MS-DRG index
Defines the logic of DRG(s) 196-198 in MDC 04.
Approximate ICD-9-CM (GEMs)
516.31 Idiopathic pulmonary fibrosis
Code annotations containing back-references to J84.112
Back-references to J84.11
- Use Additional:
M31.11 Hematopoietic stem cell transplantation-associated thrombotic microangiopathy [HSCT-TMA] ("idiopathic interstitial pneumonia (J84.11-)")
Back-references to J84
- Code Also:
I27.23 Pulmonary hypertension due to lung diseases and hypoxia ("interstitial lung disease (J84.-)")
Diagnosis Index entries for J84.112
- Alveolitis › fibrosing (cryptogenic) (idiopathic)
- Fibrosis, fibrotic › lung (atrophic) (chronic) (confluent) (massive) (perialveolar) (peribronchial) › idiopathic
- Fibrosis, fibrotic › pulmonary › idiopathic
- Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved) › interstitial › usual
- Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved) › interstitial › usual › idiopathic
Nearby codes
J84.09 Other alveolar and parieto-alveolar conditionsJ84.1 Other interstitial pulmonary diseases with fibrosisJ84.10 Pulmonary fibrosis, unspecifiedJ84.11 Idiopathic interstitial pneumoniaJ84.111 Idiopathic interstitial pneumonia, not otherwise specifiedJ84.112 Idiopathic pulmonary fibrosis (this code)J84.113 Idiopathic non-specific interstitial pneumonitisJ84.114 Acute interstitial pneumonitisJ84.115 Respiratory bronchiolitis interstitial lung diseaseJ84.116 Cryptogenic organizing pneumoniaJ84.117 Desquamative interstitial pneumonia