ICD-10-CM › J84 › J84.8 J84.89 Other specified interstitial pulmonary diseasesBillable ICD-10-CM code, FY2026.
Applicable to Endogenous lipoid pneumonia Interstitial pneumonitis Non-specific interstitial pneumonitis NOS Organizing pneumonia NOS Excludes1 (never code together) cryptogenic organizing pneumonia (J84.116) idiopathic non-specific interstitial pneumonitis (J84.113) lipoid pneumonia, exogenous or unspecified (J69.1) lymphoid interstitial pneumonia (J84.2) Code first , if applicable: poisoning due to drug or toxin (T51-T65 with fifth or sixth character to indicate intent), for toxic pneumonopathy underlying cause of pneumonopathy, if known Use additional code code, for adverse effect, to identify drug (T36-T50 with fifth or sixth character 5), if drug-induced Applies from J84 Other interstitial pulmonary diseases Excludes1 (never code together) drug-induced interstitial lung disorders (J70.2-J70.4) interstitial emphysema (J98.2) Excludes2 (not included here) lung diseases due to external agents (J60-J70) Code also , if applicable, associated condition Applies from J84.8 Other specified interstitial pulmonary diseases Excludes1 (never code together) exogenous lipoid pneumonia (J69.1) unspecified lipoid pneumonia (J69.1) Risk adjustment (HCC) CMS-HCC V28: HCC 280 — Chronic Obstructive Pulmonary Disease, Interstitial Lung Disorders, and Other Chronic Lung Disorders CMS-HCC V22: HCC 112 — Fibrosis of Lung and Other Chronic Lung Disorders RxHCC V08: HCC 227 — Pulmonary Fibrosis, Except Idiopathic ESRD V24: HCC 112 MS-DRG index Defines the logic of DRG(s) 196-198 in MDC 04.
Approximate ICD-9-CM (GEMs) 515 Postinflammatory pulmonary fibrosis (approximate)Code annotations containing back-references to J84.89 Back-references to J84.89 Type 1 Excludes: J69.1 Pneumonitis due to inhalation of oils and essences ("endogenous lipoid pneumonia (J84.89)") Type 1 Excludes: J84.113 Idiopathic non-specific interstitial pneumonitis ("non-specific interstitial pneumonia NOS, or due to known underlying cause (J84.89)") Type 1 Excludes: J84.116 Cryptogenic organizing pneumonia ("organizing pneumonia NOS, or due to known underlying cause (J84.89)") Code Also: M34.81 Systemic sclerosis with lung involvement ("other interstitial pulmonary diseases (J84.89)") Back-references to J84 Code Also: I27.23 Pulmonary hypertension due to lung diseases and hypoxia ("interstitial lung disease (J84.-)") Diagnosis Index entries for J84.89 BOOP (bronchiolitis obliterans organized pneumonia) Bronchiolitis (acute) (infective) (subacute) › obliterans › with organizing pneumonia (BOOP) Disease, diseased › lung › interstitial › specified NEC Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved) › bronchiolitis obliterans organized (BOOP) Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved) › broncho-, bronchial (confluent) (croupous) (diffuse) (disseminated) (hemorrhagic) (involving lobes) (lobar) (terminal) › lipid, lipoid › endogenous Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved) › cholesterol Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved) › interstitial › non-specific Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved) › lipid, lipoid (exogenous) › endogenous Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved) › organizing Pneumonitis (acute) (primary) › cholesterol Pneumonitis (acute) (primary) › interstitial (chronic) Pneumonitis (acute) (primary) › interstitial (chronic) › non-specific Nearby codes J84.84 Other interstitial lung diseases of childhoodJ84.841 Neuroendocrine cell hyperplasia of infancyJ84.842 Pulmonary interstitial glycogenosisJ84.843 Alveolar capillary dysplasia with vein misalignmentJ84.848 Other interstitial lung diseases of childhoodJ84.89 Other specified interstitial pulmonary diseases (this code)J84.9 Interstitial pulmonary disease, unspecified