M34.81 Systemic sclerosis with lung involvement

Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis.

Code also

• if applicable:
• other interstitial pulmonary diseases (J84.89)
• secondary pulmonary arterial hypertension (I27.21)

Applies from M34 Systemic sclerosis [scleroderma]

Excludes1 (never code together)

• circumscribed scleroderma (L94.0)
• neonatal scleroderma (P83.88)

Risk adjustment (HCC)

• CMS-HCC V28: HCC 278 — Idiopathic Pulmonary Fibrosis and Lung Involvement in Systemic Sclerosis
• CMS-HCC V22: HCC 112 — Fibrosis of Lung and Other Chronic Lung Disorders
• RxHCC V08: HCC 226 — Idiopathic Pulmonary Fibrosis and Systemic Sclerosis with Lung Involvement
• ESRD V24: HCC 112

MS-DRG index

Defines the logic of DRG(s) 196-198 in MDC 04.

Approximate ICD-9-CM (GEMs)

• 517.2 Lung involvement in systemic sclerosis (approximate)
• 710.1 Systemic sclerosis (approximate)

Code annotations containing back-references to M34.81

Back-references to M34.81

• Type 1 Excludes: J99 Respiratory disorders in diseases classified elsewhere ("systemic sclerosis (M34.81)")

Back-references to M34

• Code Also: I27.21 Secondary pulmonary arterial hypertension ("systemic sclerosis (M34.-)")
• Type 2 Excludes: I77 Other disorders of arteries and arterioles ("collagen (vascular) diseases (M30-M36)")
• Type 2 Excludes: J82 Pulmonary eosinophilia, not elsewhere classified ("pulmonary eosinophilia due to systemic connective tissue disorders (M30-M36)")
• Code First: J84.170 Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere ("systemic connective tissue disorders (M30-M36)")
• Code First: K31.84 Gastroparesis ("scleroderma (M34.-)")
• Type 1 Excludes: L93 Lupus erythematosus ("scleroderma (M34.-)")
• Type 1 Excludes: L94 Other localized connective tissue disorders ("systemic connective tissue disorders (M30-M36)")

Diagnosis Index entries for M34.81

• Disease, diseased › lung › in › systemic › sclerosis
• Sclerosis, sclerotic › systemic › with › lung involvement

Nearby codes

• M34 Systemic sclerosis [scleroderma]
• M34.0 Progressive systemic sclerosis
• M34.1 CR(E)ST syndrome
• M34.2 Systemic sclerosis induced by drug and chemical
• M34.8 Other forms of systemic sclerosis
• M34.81 Systemic sclerosis with lung involvement (this code)
• M34.82 Systemic sclerosis with myopathy
• M34.83 Systemic sclerosis with polyneuropathy
• M34.89 Other systemic sclerosis
• M34.9 Systemic sclerosis, unspecified