M34.0 Progressive systemic sclerosis

Billable ICD-10-CM code, FY2026.

Applies from M34 Systemic sclerosis [scleroderma]

Excludes1 (never code together)

• circumscribed scleroderma (L94.0)
• neonatal scleroderma (P83.88)

Risk adjustment (HCC)

• CMS-HCC V28: HCC 93 — Rheumatoid Arthritis and Other Specified Inflammatory Rheumatic Disorders
• CMS-HCC V22: HCC 40 — Rheumatoid Arthritis and Inflammatory Connective Tissue Disease
• RxHCC V08: HCC 82 — Systemic Sclerosis
• ESRD V24: HCC 40

MS-DRG index

Defines the logic of DRG(s) 545-547 in MDC 08.

Approximate ICD-9-CM (GEMs)

• 710.1 Systemic sclerosis (approximate)

Code annotations containing back-references to M34.0

Back-references to M34.0

• Code First: J84.178 Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere ("progressive systemic sclerosis (M34.0)")

Back-references to M34

• Code Also: I27.21 Secondary pulmonary arterial hypertension ("systemic sclerosis (M34.-)")
• Type 2 Excludes: I77 Other disorders of arteries and arterioles ("collagen (vascular) diseases (M30-M36)")
• Type 2 Excludes: J82 Pulmonary eosinophilia, not elsewhere classified ("pulmonary eosinophilia due to systemic connective tissue disorders (M30-M36)")
• Code First: J84.170 Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere ("systemic connective tissue disorders (M30-M36)")
• Code First: K31.84 Gastroparesis ("scleroderma (M34.-)")
• Type 1 Excludes: L93 Lupus erythematosus ("scleroderma (M34.-)")
• Type 1 Excludes: L94 Other localized connective tissue disorders ("systemic connective tissue disorders (M30-M36)")

Diagnosis Index entries for M34.0

• Sclerosis, sclerotic › progressive, systemic
• Sclerosis, sclerotic › systemic › progressive

Nearby codes

• M34 Systemic sclerosis [scleroderma]
• M34.0 Progressive systemic sclerosis (this code)
• M34.1 CR(E)ST syndrome
• M34.2 Systemic sclerosis induced by drug and chemical
• M34.8 Other forms of systemic sclerosis
• M34.81 Systemic sclerosis with lung involvement
• M34.82 Systemic sclerosis with myopathy