ICD-10-CM › J99 J99 Respiratory disorders in diseases classified elsewhereBillable ICD-10-CM code, FY2026.
Excludes1 (never code together) respiratory disorders in: amebiasis (A06.5) blastomycosis (B40.0-B40.2) candidiasis (B37.1) coccidioidomycosis (B38.0-B38.2) cystic fibrosis with pulmonary manifestations (E84.0) dermatomyositis (M33.01, M33.11) histoplasmosis (B39.0-B39.2) late syphilis (A52.72, A52.73) polymyositis (M33.21) Sjögren syndrome (M35.02) systemic lupus erythematosus (M32.13) systemic sclerosis (M34.81) Wegener's granulomatosis (M31.30-M31.31) Code first underlying disease, such as: amyloidosis (E85.-) ankylosing spondylitis (M45.-) congenital syphilis (A50.-) cryoglobulinemia (D89.1) early congenital syphilis (A50.0-) plasminogen deficiency (E88.02) schistosomiasis (B65.0-B65.9) Applies from J99 Respiratory disorders in diseases classified elsewhere Excludes1 (never code together) respiratory disorders in: amebiasis (A06.5) blastomycosis (B40.0-B40.2) candidiasis (B37.1) coccidioidomycosis (B38.0-B38.2) cystic fibrosis with pulmonary manifestations (E84.0) dermatomyositis (M33.01, M33.11) histoplasmosis (B39.0-B39.2) late syphilis (A52.72, A52.73) polymyositis (M33.21) Sjögren syndrome (M35.02) systemic lupus erythematosus (M32.13) systemic sclerosis (M34.81) Wegener's granulomatosis (M31.30-M31.31) Code first underlying disease, such as: amyloidosis (E85.-) ankylosing spondylitis (M45.-) congenital syphilis (A50.-) cryoglobulinemia (D89.1) early congenital syphilis (A50.0-) plasminogen deficiency (E88.02) schistosomiasis (B65.0-B65.9) Risk adjustment (HCC) CMS-HCC V28: HCC 280 — Chronic Obstructive Pulmonary Disease, Interstitial Lung Disorders, and Other Chronic Lung Disorders CMS-HCC V22: HCC 112 — Fibrosis of Lung and Other Chronic Lung Disorders RxHCC V08: HCC 227 — Pulmonary Fibrosis, Except Idiopathic ESRD V24: HCC 112 MS-DRG index Defines the logic of DRG(s) 196-198 in MDC 04.
Approximate ICD-9-CM (GEMs) 517.8 Lung involvement in other diseases classified elsewhere (approximate)Medicare Code Edits (MCE v43.1 (April 2026)) Code annotations containing back-references to J99 Back-references to J99 Use Additional: E88.02 Plasminogen deficiency ("respiratory disorder related to plasminogen deficiency (J99)") Back-references to J99 Use Additional: E88.02 Plasminogen deficiency ("respiratory disorder related to plasminogen deficiency (J99)") Diagnosis Index entries for J99 Amyloidosis (generalized) (primary) › with lung involvement Amyloidosis (generalized) (primary) › pulmonary Amyloidosis (generalized) (primary) › subglottic Bilharziasis › pulmonary NOS Bronchomycosis NOS Cryoglobulinemia (essential) (idiopathic) (mixed) (primary) (purpura) (secondary) (vasculitis) › with lung involvement Cyst (colloid) (mucous) (simple) (retention) › hydatid › lung NEC Disease, diseased › lung › in › amyloidosis Laryngitis (acute) (edematous) (fibrinous) (infective) (infiltrative) (malignant) (membranous) (phlegmonous) (pneumococcal) (pseudomembranous) (septic) (subglottic) (suppurative) (ulcerative) › syphilitic (late) › congenital Laryngitis (acute) (edematous) (fibrinous) (infective) (infiltrative) (malignant) (membranous) (phlegmonous) (pneumococcal) (pseudomembranous) (septic) (subglottic) (suppurative) (ulcerative) › syphilitic (late) › congenital › early Laryngotracheitis (acute) (Infectional) (infective) (viral) › syphilitic (late) › congenital Laryngotracheitis (acute) (Infectional) (infective) (viral) › syphilitic (late) › congenital › early Pneumomycosis Rhinitis (atrophic) (catarrhal) (chronic) (croupous) (fibrinous) (granulomatous) (hyperplastic) (hypertrophic) (membranous) (obstructive) (purulent) (suppurative) (ulcerative) › syphilitic › congenital Schistosomiasis › lung NEC Schistosomiasis › pulmonary NEC Snuffles (non-syphilitic) › syphilitic (infant) Spondylitis (chronic) › ankylosing (chronic) › with lung involvement Stenosis, stenotic (cicatricial) › larynx › syphilitic › congenital Stricture › larynx › syphilitic › congenital Stricture › nostril (anterior) (posterior) › syphilitic › congenital Nearby codes J99 Respiratory disorders in diseases classified elsewhere (this code)