K83.01 Primary sclerosing cholangitis

Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis.

Applies from K83 Other diseases of biliary tract

Excludes1 (never code together)

• postcholecystectomy syndrome (K91.5)

Excludes2 (not included here)

• conditions involving the gallbladder (K81-K82)
• conditions involving the cystic duct (K81-K82)

Applies from K83.0 Cholangitis

Excludes1 (never code together)

• cholangitic liver abscess (K75.0)
• cholangitis with choledocholithiasis (K80.3-, K80.4-)

Excludes2 (not included here)

• chronic nonsuppurative destructive cholangitis (K74.3)
• primary biliary cholangitis (K74.3)
• primary biliary cirrhosis (K74.3)

Risk adjustment (HCC)

• CMS-HCC V28: HCC 68 — Cholangitis and Obstruction of Bile Duct Without Gallstones

MS-DRG index

Defines the logic of DRG(s) 444-446 in MDC 07.

Code annotations containing back-references to K83.01

Back-references to K83.01

• Type 2 Excludes: K74.3 Primary biliary cirrhosis ("primary sclerosing cholangitis (K83.01)")

Diagnosis Index entries for K83.01

• Cholangitis (ascending) (recurrent) (secondary) (stenosing) (suppurative) › primary › sclerosing

Nearby codes

• K83 Other diseases of biliary tract
• K83.0 Cholangitis
• K83.01 Primary sclerosing cholangitis (this code)
• K83.09 Other cholangitis
• K83.1 Obstruction of bile duct
• K83.2 Perforation of bile duct
• K83.3 Fistula of bile duct
• K83.4 Spasm of sphincter of Oddi