M31.7 Microscopic polyangiitisBillable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis.
Defines the logic of DRG(s) 545-547 in MDC 08.
446.0 Polyarteritis nodosa (approximate)I77.82 Antineutrophilic cytoplasmic antibody [ANCA] vasculitis ("microscopic polyangiitis (M31.7)")M30 Polyarteritis nodosa and related conditions ("microscopic polyarteritis (M31.7)")N08 Glomerular disorders in diseases classified elsewhere ("microscopic polyangiitis (M31.7)")I77 Other disorders of arteries and arterioles ("collagen (vascular) diseases (M30-M36)")J82 Pulmonary eosinophilia, not elsewhere classified ("pulmonary eosinophilia due to systemic connective tissue disorders (M30-M36)")J84.170 Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere ("systemic connective tissue disorders (M30-M36)")L94 Other localized connective tissue disorders ("systemic connective tissue disorders (M30-M36)")M31.30 Wegener's granulomatosis without renal involvementM31.31 Wegener's granulomatosis with renal involvementM31.4 Aortic arch syndrome [Takayasu]M31.5 Giant cell arteritis with polymyalgia rheumaticaM31.6 Other giant cell arteritisM31.7 Microscopic polyangiitis (this code)M31.8 Other specified necrotizing vasculopathiesM31.9 Necrotizing vasculopathy, unspecified