M31.31 Wegener's granulomatosis with renal involvementBillable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis.
Defines the logic of DRG(s) 542-544 in MDC 08.
446.4 Wegener's granulomatosis (approximate)J99 Respiratory disorders in diseases classified elsewhere ("Wegener's granulomatosis (M31.30-M31.31)")N08 Glomerular disorders in diseases classified elsewhere ("Wegener's granulomatosis (M31.31)")I77.82 Antineutrophilic cytoplasmic antibody [ANCA] vasculitis ("granulomatosis with polyangiitis (M31.3-)")L95 Vasculitis limited to skin, not elsewhere classified ("Wegener's granulomatosis (M31.3-)")I77 Other disorders of arteries and arterioles ("collagen (vascular) diseases (M30-M36)")J82 Pulmonary eosinophilia, not elsewhere classified ("pulmonary eosinophilia due to systemic connective tissue disorders (M30-M36)")J84.170 Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere ("systemic connective tissue disorders (M30-M36)")L94 Other localized connective tissue disorders ("systemic connective tissue disorders (M30-M36)")M31.11 Hematopoietic stem cell transplantation-associated thrombotic microangiopathy [HSCT-TMA]M31.19 Other thrombotic microangiopathyM31.2 Lethal midline granulomaM31.3 Wegener's granulomatosisM31.30 Wegener's granulomatosis without renal involvementM31.31 Wegener's granulomatosis with renal involvement (this code)M31.4 Aortic arch syndrome [Takayasu]M31.5 Giant cell arteritis with polymyalgia rheumaticaM31.6 Other giant cell arteritisM31.7 Microscopic polyangiitisM31.8 Other specified necrotizing vasculopathies