M35.01 Sjögren syndrome with keratoconjunctivitis

Billable ICD-10-CM code, FY2026.

Applies from M35 Other systemic involvement of connective tissue

Excludes1 (never code together)

• reactive perforating collagenosis (L87.1)

Applies from M35.0 Sjögren syndrome

Applicable to

• Sicca syndrome

Excludes1 (never code together)

• dry mouth, unspecified (R68.2)

Use additional code

• code to identify associated manifestations

Risk adjustment (HCC)

• CMS-HCC V22: HCC 40 — Rheumatoid Arthritis and Inflammatory Connective Tissue Disease
• RxHCC V08: HCC 84 — Systemic Lupus Erythematosus and Other Systemic Connective Tissue Disorders
• ESRD V24: HCC 40

MS-DRG index

Defines the logic of DRG(s) 545-547 in MDC 08.

Approximate ICD-9-CM (GEMs)

• 710.2 Sicca syndrome (approximate)

Code annotations containing back-references to M35.01

Back-references to M35.01

• Type 1 Excludes: H16.22 Keratoconjunctivitis sicca, not specified as Sjögren's ("Sjögren's syndrome (M35.01)")

Back-references to M35.0

• Code Also: I27.21 Secondary pulmonary arterial hypertension ("Sjögren syndrome (M35.0-)")
• Type 1 Excludes: K11.8 Other diseases of salivary glands ("Sjögren syndrome (M35.0-)")
• Type 1 Excludes: R68.2 Dry mouth, unspecified ("dry mouth due to Sjögren syndrome (M35.0-)")

Back-references to M35

• Type 2 Excludes: I77 Other disorders of arteries and arterioles ("collagen (vascular) diseases (M30-M36)")
• Type 2 Excludes: J82 Pulmonary eosinophilia, not elsewhere classified ("pulmonary eosinophilia due to systemic connective tissue disorders (M30-M36)")
• Code First: J84.170 Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere ("systemic connective tissue disorders (M30-M36)")
• Type 1 Excludes: L94 Other localized connective tissue disorders ("systemic connective tissue disorders (M30-M36)")

Diagnosis Index entries for M35.01

• Syndrome › Sjögren › with › keratoconjunctivitis

Nearby codes

• M35 Other systemic involvement of connective tissue
• M35.0 Sjogren syndrome
• M35.00 Sjogren syndrome, unspecified
• M35.01 Sjogren syndrome with keratoconjunctivitis (this code)
• M35.02 Sjogren syndrome with lung involvement
• M35.03 Sjogren syndrome with myopathy
• M35.04 Sjogren syndrome with tubulo-interstitial nephropathy
• M35.05 Sjogren syndrome with inflammatory arthritis
• M35.06 Sjogren syndrome with peripheral nervous system involvement