M35.0 Sjögren syndrome

Non-billable header with 13 child codes.

Applicable to

• Sicca syndrome

Excludes1 (never code together)

• dry mouth, unspecified (R68.2)

Use additional code

• code to identify associated manifestations

Applies from M35 Other systemic involvement of connective tissue

Excludes1 (never code together)

• reactive perforating collagenosis (L87.1)

Codes under M35.0

• M35.00 Sjögren syndrome, unspecified
• M35.01 Sjögren syndrome with keratoconjunctivitis
• M35.02 Sjögren syndrome with lung involvement
• M35.03 Sjögren syndrome with myopathy
• M35.04 Sjögren syndrome with tubulo-interstitial nephropathy
• M35.05 Sjögren syndrome with inflammatory arthritis
• M35.06 Sjögren syndrome with peripheral nervous system involvement
• M35.07 Sjögren syndrome with central nervous system involvement
• M35.08 Sjögren syndrome with gastrointestinal involvement
• M35.0A Sjögren syndrome with glomerular disease
• M35.0B Sjögren syndrome with vasculitis
• M35.0C Sjögren syndrome with dental involvement
• M35.09 Sjögren syndrome with other organ involvement

Code annotations containing back-references to M35.0

Back-references to M35.0

• Code Also: I27.21 Secondary pulmonary arterial hypertension ("Sjögren syndrome (M35.0-)")
• Type 1 Excludes: K11.8 Other diseases of salivary glands ("Sjögren syndrome (M35.0-)")
• Type 1 Excludes: R68.2 Dry mouth, unspecified ("dry mouth due to Sjögren syndrome (M35.0-)")

Back-references to M35

• Type 2 Excludes: I77 Other disorders of arteries and arterioles ("collagen (vascular) diseases (M30-M36)")
• Type 2 Excludes: J82 Pulmonary eosinophilia, not elsewhere classified ("pulmonary eosinophilia due to systemic connective tissue disorders (M30-M36)")
• Code First: J84.170 Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere ("systemic connective tissue disorders (M30-M36)")
• Type 1 Excludes: L94 Other localized connective tissue disorders ("systemic connective tissue disorders (M30-M36)")

Diagnosis Index entries for M35.0

• Keratoconjunctivitis › sicca (Sjögren's)

Nearby codes

• M35 Other systemic involvement of connective tissue
• M35.0 Sjogren syndrome (this code)
• M35.00 Sjogren syndrome, unspecified
• M35.01 Sjogren syndrome with keratoconjunctivitis
• M35.02 Sjogren syndrome with lung involvement
• M35.03 Sjogren syndrome with myopathy
• M35.04 Sjogren syndrome with tubulo-interstitial nephropathy