M35.0B Sjögren syndrome with vasculitis

Billable ICD-10-CM code, FY2026.

Applies from M35 Other systemic involvement of connective tissue

Excludes1 (never code together)

• reactive perforating collagenosis (L87.1)

Applies from M35.0 Sjögren syndrome

Applicable to

• Sicca syndrome

Excludes1 (never code together)

• dry mouth, unspecified (R68.2)

Use additional code

• code to identify associated manifestations

Risk adjustment (HCC)

• CMS-HCC V22: HCC 40 — Rheumatoid Arthritis and Inflammatory Connective Tissue Disease
• RxHCC V08: HCC 84 — Systemic Lupus Erythematosus and Other Systemic Connective Tissue Disorders
• ESRD V24: HCC 40

MS-DRG index

Defines the logic of DRG(s) 545-547 in MDC 08.

Code annotations containing back-references to M35.0B

Back-references to M35.0

• Code Also: I27.21 Secondary pulmonary arterial hypertension ("Sjögren syndrome (M35.0-)")
• Type 1 Excludes: K11.8 Other diseases of salivary glands ("Sjögren syndrome (M35.0-)")
• Type 1 Excludes: R68.2 Dry mouth, unspecified ("dry mouth due to Sjögren syndrome (M35.0-)")

Back-references to M35

• Type 2 Excludes: I77 Other disorders of arteries and arterioles ("collagen (vascular) diseases (M30-M36)")
• Type 2 Excludes: J82 Pulmonary eosinophilia, not elsewhere classified ("pulmonary eosinophilia due to systemic connective tissue disorders (M30-M36)")
• Code First: J84.170 Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere ("systemic connective tissue disorders (M30-M36)")
• Type 1 Excludes: L94 Other localized connective tissue disorders ("systemic connective tissue disorders (M30-M36)")

Diagnosis Index entries for M35.0B

• Syndrome › Sjögren › with › vasculitis

Nearby codes

• M35.05 Sjogren syndrome with inflammatory arthritis
• M35.06 Sjogren syndrome with peripheral nervous system involvement
• M35.07 Sjogren syndrome with central nervous system involvement
• M35.08 Sjogren syndrome with gastrointestinal involvement
• M35.0A Sjogren syndrome with glomerular disease
• M35.0B Sjogren syndrome with vasculitis (this code)
• M35.0C Sjogren syndrome with dental involvement
• M35.09 Sjogren syndrome with other organ involvement
• M35.1 Other overlap syndromes
• M35.2 Behcet's disease
• M35.3 Polymyalgia rheumatica