N01.9 Rapidly progressive nephritic syndrome with unspecified morphologic changes

Billable ICD-10-CM code, FY2026. Acts as a Major Complication or Comorbidity (MCC) as a secondary diagnosis.

Applies from N01 Rapidly progressive nephritic syndrome

Includes

• rapidly progressive glomerular disease
• rapidly progressive glomerulonephritis
• rapidly progressive nephritis

Excludes1 (never code together)

• nephritic syndrome NOS (N05.-)

MS-DRG index

Defines the logic of DRG(s) 698-700 in MDC 11.

Approximate ICD-9-CM (GEMs)

• 580.4 Acute glomerulonephritis with lesion of rapidly progressive glomerulonephritis (approximate)

Diagnosis Index entries for N01.9

• Disease, diseased › glomerular › rapidly progressive
• Disease, diseased › renal (functional) (pelvis) › rapidly progressive
• Disease, diseased › renal (functional) (pelvis) › subacute
• Glomerulonephritis › poststreptococcal NEC › rapidly progressive
• Glomerulonephritis › rapidly progressive
• Glomerulonephritis › subacute
• Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic) › poststreptococcal › rapidly progressive
• Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic) › rapidly progressive
• Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic) › subacute
• Syndrome › nephritic › rapidly progressive

Nearby codes

• N01.4 Rapidly progressive nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis
• N01.5 Rapidly progressive nephritic syndrome with diffuse mesangiocapillary glomerulonephritis
• N01.6 Rapidly progressive nephritic syndrome with dense deposit disease
• N01.7 Rapidly progressive nephritic syndrome with diffuse crescentic glomerulonephritis
• N01.8 Rapidly progressive nephritic syndrome with other morphologic changes
• N01.9 Rapidly progressive nephritic syndrome with unspecified morphologic changes (this code)
• N01.A Rapidly progressive nephritic syndrome with C3 glomerulonephritis