N01.A Rapidly progressive nephritic syndrome with C3 glomerulonephritis

Billable ICD-10-CM code, FY2026. Acts as a Major Complication or Comorbidity (MCC) as a secondary diagnosis.

Applicable to

• Rapidly progressive nephritic syndrome with C3 glomerulopathy, NOS

Excludes1 (never code together)

• Rapidly progressive nephritic syndrome (with C3 glomerulopathy) with dense deposit disease (N01.6)

Applies from N01 Rapidly progressive nephritic syndrome

Includes

• rapidly progressive glomerular disease
• rapidly progressive glomerulonephritis
• rapidly progressive nephritis

Excludes1 (never code together)

• nephritic syndrome NOS (N05.-)

MS-DRG index

Defines the logic of DRG(s) 698-700 in MDC 11.

Code annotations containing back-references to N01.A

Back-references to N01.A

• Type 1 Excludes: N01.5 Rapidly progressive nephritic syndrome with diffuse mesangiocapillary glomerulonephritis ("Rapidly progressive nephritic syndrome with C3 glomerulonephritis (N01.A)")
• Type 1 Excludes: N01.5 Rapidly progressive nephritic syndrome with diffuse mesangiocapillary glomerulonephritis ("Rapidly progressive nephritic syndrome with C3 glomerulopathy (N01.A)")

Diagnosis Index entries for N01.A

• Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic) › rapidly progressive › with › C3 › glomerulonephritis
• Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic) › rapidly progressive › with › C3 › glomerulopathy

Nearby codes

• N01.5 Rapidly progressive nephritic syndrome with diffuse mesangiocapillary glomerulonephritis
• N01.6 Rapidly progressive nephritic syndrome with dense deposit disease
• N01.7 Rapidly progressive nephritic syndrome with diffuse crescentic glomerulonephritis
• N01.8 Rapidly progressive nephritic syndrome with other morphologic changes
• N01.9 Rapidly progressive nephritic syndrome with unspecified morphologic changes
• N01.A Rapidly progressive nephritic syndrome with C3 glomerulonephritis (this code)