N04.6 Nephrotic syndrome with dense deposit disease

Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis.

Applicable to

• Nephrotic syndrome with C3 glomerulopathy with dense deposit disease
• Nephrotic syndrome with membranoproliferative glomerulonephritis, type 2

Applies from N04 Nephrotic syndrome

Includes

• congenital nephrotic syndrome
• lipoid nephrosis

MS-DRG index

Defines the logic of DRG(s) 698-700 in MDC 11.

Approximate ICD-9-CM (GEMs)

• 581.2 Nephrotic syndrome with lesion of membranoproliferative glomerulonephritis (approximate)

Code annotations containing back-references to N04.6

Back-references to N04.6

• Type 1 Excludes: N04.A Nephrotic syndrome with C3 glomerulonephritis ("Nephrotic syndrome (with C3 glomerulopathy) with dense deposit disease (N04.6)")

Back-references to N04

• Type 1 Excludes: Q63 Other congenital malformations of kidney ("congenital nephrotic syndrome (N04.-)")

Diagnosis Index entries for N04.6

• Syndrome › nephrotic (congenital) › with › C3 › glomerulopathy › with dense deposit disease
• Syndrome › nephrotic (congenital) › with › dense deposit disease

Nearby codes

• N04.22 Secondary membranous nephropathy with nephrotic syndrome
• N04.29 Other nephrotic syndrome with diffuse membranous glomerulonephritis
• N04.3 Nephrotic syndrome with diffuse mesangial proliferative glomerulonephritis
• N04.4 Nephrotic syndrome with diffuse endocapillary proliferative glomerulonephritis
• N04.5 Nephrotic syndrome with diffuse mesangiocapillary glomerulonephritis
• N04.6 Nephrotic syndrome with dense deposit disease (this code)
• N04.7 Nephrotic syndrome with diffuse crescentic glomerulonephritis
• N04.8 Nephrotic syndrome with other morphologic changes
• N04.9 Nephrotic syndrome with unspecified morphologic changes
• N04.A Nephrotic syndrome with C3 glomerulonephritis
• N04.B Nephrotic syndrome with immune complex membranoproliferative glomerulonephritis (IC-MPGN)