N04.A Nephrotic syndrome with C3 glomerulonephritis

Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis.

Applicable to

• Nephrotic syndrome with C3 glomerulopathy

Excludes1 (never code together)

• Nephrotic syndrome (with C3 glomerulopathy) with dense deposit disease (N04.6)

Applies from N04 Nephrotic syndrome

Includes

• congenital nephrotic syndrome
• lipoid nephrosis

MS-DRG index

Defines the logic of DRG(s) 698-700 in MDC 11.

Code annotations containing back-references to N04.A

Back-references to N04.A

• Type 1 Excludes: N04.5 Nephrotic syndrome with diffuse mesangiocapillary glomerulonephritis ("Nephrotic syndrome with C3 glomerulonephritis (N04.A)")
• Type 1 Excludes: N04.5 Nephrotic syndrome with diffuse mesangiocapillary glomerulonephritis ("Nephrotic syndrome with C3 glomerulopathy (N04.A)")

Back-references to N04

• Type 1 Excludes: Q63 Other congenital malformations of kidney ("congenital nephrotic syndrome (N04.-)")

Diagnosis Index entries for N04.A

• Syndrome › nephrotic (congenital) › with › C3 › glomerulonephritis
• Syndrome › nephrotic (congenital) › with › C3 › glomerulopathy

Nearby codes

• N04.5 Nephrotic syndrome with diffuse mesangiocapillary glomerulonephritis
• N04.6 Nephrotic syndrome with dense deposit disease
• N04.7 Nephrotic syndrome with diffuse crescentic glomerulonephritis
• N04.8 Nephrotic syndrome with other morphologic changes
• N04.9 Nephrotic syndrome with unspecified morphologic changes
• N04.A Nephrotic syndrome with C3 glomerulonephritis (this code)
• N04.B Nephrotic syndrome with immune complex membranoproliferative glomerulonephritis (IC-MPGN)
• N04.B1 Nephrotic syndrome with idiopathic immune complex membranoproliferative glomerulonephritis (IC-MPGN)
• N04.B2 Nephrotic syndrome with secondary immune complex membranoproliferative glomerulonephritis (IC-MPGN)