Billable ICD-10-CM code, FY2026. Acts as a Major Complication or Comorbidity (MCC) as a secondary diagnosis. Exempt from present-on-admission (POA) reporting.
Applicable to
Persistent truncus arteriosus
Excludes1 (never code together)
aortic septal defect (Q21.4)
Applies from Q20 Congenital malformations of cardiac chambers and connections
Excludes1 (never code together)
dextrocardia with situs inversus (Q89.3)
mirror-image atrial arrangement with situs inversus (Q89.3)
Risk adjustment (HCC)
RxHCC V08: HCC 191 — Ventricular Septal Defect and Major Congenital Heart Disorders
MS-DRG index
Defines the logic of DRG(s) 306-307 in MDC 05.
Approximate ICD-9-CM (GEMs)
745.0 Common truncus
Code annotations containing back-references to Q20.0
Back-references to Q20.0
Use Additional: Q87.88 CTNNB1 syndrome ("congenital heart malformations (Q20.0-Q24.9)")