Q25.21 Interruption of aortic archBillable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis. Exempt from present-on-admission (POA) reporting.
Defines the logic of DRG(s) 306-307 in MDC 05.
747.11 Interruption of aortic archI27.21 Secondary pulmonary arterial hypertension ("congenital heart disease (Q20-Q28)")P29 Cardiovascular disorders originating in the perinatal period ("congenital malformations of the circulatory system (Q20-Q28)")Z71.87 Encounter for pediatric-to-adult transition counseling ("congenital malformations of the circulatory system (Q20-Q28)")Q25 Congenital malformations of great arteriesQ25.0 Patent ductus arteriosusQ25.1 Coarctation of aortaQ25.2 Atresia of aortaQ25.21 Interruption of aortic arch (this code)Q25.29 Other atresia of aortaQ25.3 Supravalvular aortic stenosisQ25.4 Other congenital malformations of aortaQ25.40 Congenital malformation of aorta unspecifiedQ25.41 Absence and aplasia of aorta