Q25.3 Supravalvular aortic stenosis

Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis. Exempt from present-on-admission (POA) reporting.

Excludes1 (never code together)

• congenital aortic stenosis NOS (Q23.0)
• congenital stenosis of aortic valve (Q23.0)

MS-DRG index

Defines the logic of DRG(s) 306-307 in MDC 05.

Approximate ICD-9-CM (GEMs)

• 747.22 Atresia and stenosis of aorta (approximate)

Code annotations containing back-references to Q25.3

Back-references to Q25.3

• Type 1 Excludes: Q23.0 Congenital stenosis of aortic valve ("supravalvular aortic stenosis (congenital) (Q25.3)")

Back-references to Q25

• Code Also: I27.21 Secondary pulmonary arterial hypertension ("congenital heart disease (Q20-Q28)")
• Type 2 Excludes: P29 Cardiovascular disorders originating in the perinatal period ("congenital malformations of the circulatory system (Q20-Q28)")
• Code Also: Z71.87 Encounter for pediatric-to-adult transition counseling ("congenital malformations of the circulatory system (Q20-Q28)")

Diagnosis Index entries for Q25.3

• Malformation (congenital) › aorta › stenosis › supravalvular
• Stenosis, stenotic (cicatricial) › aorta (ascending) (supraventricular) (congenital) › supravalvular
• Stricture › aorta (ascending) (congenital) › supravalvular, congenital

Nearby codes

• Q25.0 Patent ductus arteriosus
• Q25.1 Coarctation of aorta
• Q25.2 Atresia of aorta
• Q25.21 Interruption of aortic arch
• Q25.29 Other atresia of aorta
• Q25.3 Supravalvular aortic stenosis (this code)
• Q25.4 Other congenital malformations of aorta
• Q25.40 Congenital malformation of aorta unspecified
• Q25.41 Absence and aplasia of aorta
• Q25.42 Hypoplasia of aorta
• Q25.43 Congenital aneurysm of aorta