Q23.0 Congenital stenosis of aortic valve

Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis. Exempt from present-on-admission (POA) reporting.

Applicable to

• Congenital aortic atresia
• Congenital aortic stenosis NOS

Excludes1 (never code together)

• congenital stenosis of aortic valve in hypoplastic left heart syndrome (Q23.4)
• congenital subaortic stenosis (Q24.4)
• supravalvular aortic stenosis (congenital) (Q25.3)

MS-DRG index

Defines the logic of DRG(s) 306-307 in MDC 05.

Approximate ICD-9-CM (GEMs)

• 746.3 Congenital stenosis of aortic valve

Code annotations containing back-references to Q23.0

Back-references to Q23.0

• Type 2 Excludes: I35 Nonrheumatic aortic valve disorders ("aortic valve disorder specified as congenital (Q23.0, Q23.1)")
• Type 1 Excludes: Q25.3 Supravalvular aortic stenosis ("congenital aortic stenosis NOS (Q23.0)")
• Type 1 Excludes: Q25.3 Supravalvular aortic stenosis ("congenital stenosis of aortic valve (Q23.0)")

Back-references to Q23

• Type 2 Excludes: I08 Multiple valve diseases ("multiple valve disease specified as nonrheumatic (I34.-, I35.-, I36.-, I37.-, I38.-, Q22.-, Q23.-, Q24.8-)")
• Code Also: I27.21 Secondary pulmonary arterial hypertension ("congenital heart disease (Q20-Q28)")
• Type 2 Excludes: P29 Cardiovascular disorders originating in the perinatal period ("congenital malformations of the circulatory system (Q20-Q28)")
• Code Also: Z71.87 Encounter for pediatric-to-adult transition counseling ("congenital malformations of the circulatory system (Q20-Q28)")

Diagnosis Index entries for Q23.0

• Anomaly, anomalous (congenital) (unspecified type) › heart › valve NEC › aortic › stenosis
• Atresia, atretic › aortic (orifice) (valve)
• Stenosis, stenotic (cicatricial) › aortic (valve) › congenital
• Stenosis, stenotic (cicatricial) › valve (cardiac) (heart) › congenital › aortic
• Stricture › heart › valve › aortic
• Stricture › valve (cardiac) (heart) › congenital › aortic

Nearby codes

• Q23 Congenital malformations of aortic and mitral valves
• Q23.0 Congenital stenosis of aortic valve (this code)
• Q23.1 Congenital insufficiency of aortic valve
• Q23.2 Congenital mitral stenosis
• Q23.3 Congenital mitral insufficiency
• Q23.4 Hypoplastic left heart syndrome
• Q23.8 Other congenital malformations of aortic and mitral valves